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Editor-in-Chief: Giuseppe Leone | Italy

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  • THE HISTORY OF DEFERIPRONE (L1) AND THE COMPLETE TREATMENT OF IRON OVERLOAD IN THALASSAEMIA The history and roles of deferiprone

    George J Kontoghiorghes, Marios Kleanthous, Christina N. Kontoghiorghe
    e2020011
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.011
    2422
    PDF: 1594
    HTML: 639
  • IRON METABOLISM IN THALASSEMIA AND SICKLE CELL DISEASE

    Raffaella Mariani, Paola Trombini, Matteo Pozzi, Alberto Piperno
    e2009006
    2009-10-27
    1640
    PDF: 652
    HTML: 43916
  • MYELODYSPLASTIC SYNDROMES AND IRON CHELATION THERAPY

    Emanuele Angelucci, Silvana Anna Maria Urru, Federica Pilo, Alberto Piperno
    e2017021
    2017-03-01
    https://doi.org/10.4084/mjhid.2017.021
    3400
    PDF: 1296
    HTML: 1908
    Fig.1: 202
    Fig. 2: 214
  • CARDIAC FUNCTION AND IRON CHELATION IN THALASSEMIA MAJOR AND INTERMEDIA: A REVIEW OF THE UNDERLYING PATHOPHYSIOLOGY AND APPROACH TO CHELATION MANAGEMENT

    Athanasios Aessopos, Vasilios Berdoukas
    e2009002
    2009-07-18
    1590
    PDF: 485
    HTML: 1443
  • A Young Adult with Unintentional Acute Parenteral Iron intoxication Treated with Oral Chelation: The Use of Liver Ferriscan.

    Vincenzo De Sanctis
    e2017008
    2017-01-01
    https://doi.org/10.4084/mjhid.2017.008
    3133
    PDF: 1020
    HTML: 1654
  • DEFERASIROX: OVER A DECADE OF EXPERIENCE IN THALASSEMIA

    Ali Taher
    e2018066
    2018-11-01
    https://doi.org/10.4084/mjhid.2018.066
    2936
    PDF: 1597
    HTML: 237
  • JUSTIFICATION OF UNIVERSAL IRON SUPPLEMENTATION FOR INFANTS 6-12 MONTHS IN REGIONS WITH A HIGH PREVALENCE OF THALASSEMIA Iron Supplementation for Infants 6-12 months in Regions with a High Prevalence of Thalassemia

    Phakatip Sinlapamongkolkul, Pacharapan Surapolchai, Vip Viprakasit
    e2023056
    2023-08-29
    https://doi.org/10.4084/MJHID.2023.056
    2262
    PDF: 613
    Suppl. Files: 284
    HTML: 175
  • THE ICET-A RECOMMENDATIONS FOR THE DIAGNOSIS AND MANAGEMENT OF DISTURBANCES OF GLUCOSE HOMEOSTASIS IN THALASSEMIA MAJOR PATIENTS

    Vincenzo De Sanctis
    e2016058
    2016-10-25
    https://doi.org/10.4084/mjhid.2016.058
    4244
    PDF: 1216
    HTML: 1199
  • IRON CHELATION THERAPY IN THALASSEMIA SYNDROMES

    Paolo Cianciulli
    e2009034
    1271
    PDF: 617
    HTML: 2320
  • TRANSIENT ELASTOGRAPHY (TE) IS A USEFUL TOOL FOR ASSESSING THE RESPONSE OF LIVER IRON CHELATION IN SICKLE CELL DISEASE PATIENTS

    SOPHIA DELICOU
    e2018049
    2018-09-01
    https://doi.org/10.4084/mjhid.2018.049
    1561
    PDF: 829
    HTML: 195
  • THERAPEUTIC VALUE OF COMBINED THERAPY WITH DEFERASIROX AND SILYMARIN ON IRON OVERLOAD IN CHILDREN WITH BETA THALASSEMIA

    adel abd elhaleim hagag
    e2013065
    2013-11-04
    https://doi.org/10.4084/mjhid.2013.065
    2656
    PDF: 835
    HTML: 14966
    Therapeutic Value of Combined Therapy with Deferasirox and Silymarin on Iron Overload in Children with Beta Thalassemia: 312
  • LIVER IRON CONTENT (LIC) IN ADULTS WITH NON-TRANSFUSION DEPENDENT SICKLE CELL DISEASE (NT-SCD). CORRELATION WITH SERUM FERRITIN AND LIVER ENZYMES CONCENTRATIONS

    Vincenzo De Sanctis
    e2017037
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.037
    3894
    PDF: 979
    HTML: 1152
  • GLUCOSE HOMEOSTASIS AND ΑSSESSMENT OF Β-CELL FUNCTION BY 3-HOUR ORAL GLUCOSE TOLERANCE (OGTT) IN PATIENTS WITH Β-THALASSEMIA MAJOR WITH SERUM FERRITIN BELOW 1,000 NG/DL: RESULTS FROM A SINGLE ICET-A CENTRE OGTT in thalassemia and iron overload

    Vincenzo De Sanctis, Ashraf Soliman, Shahina Daar, Ploutarchos Tzoulis , Salvatore Di Maio, Christos Kattamis
    e2023006
    2023-01-01
    https://doi.org/10.4084/MJHID.2023.006
    3945
    PDF: 1114
    HTML: 460
  • SALIVA IRON AND FERRITIN LEVELS IN PATIENTS WITH THALASSEMIA AND IRON DEFICIENCY ANEMIA

    Duran Canatan, Sevgi Kosaci Akdeniz
    e2012051
    2012-08-09
    https://doi.org/10.4084/mjhid.2012.051
    2948
    PDF: 1481
    HTML: 10901
  • ASSOCİATİON BETWEEN IRON OVERLOAD AND GLUCOSE METABOLİSM İN CHİLDREN AND YOUTH WİTH TRANSFUSİON-DEPENDENT BETA THALASSEMİA: THE ROLE OF CHELATİON THERAPY

    Deniz Guven, Dr. İncefidan, Dr. Kazanci, Dr. Ozlem Kara
    2026-02-28
    https://doi.org/10.4084/MJHID.2026.017
    658
    PDF: 545
    HTML: 72
  • ACQUIRED HYPOGONADOTROPIC HYPOGONADISM (AHH) IN THALASSAEMIA MAJOR PATIENTS: AN UNDERDIAGNOSED CONDITION?

    Vincenzo De Sanctis
    e2016001
    2016-01-01
    https://doi.org/10.4084/mjhid.2016.001
    5182
    PDF: 1307
    HTML: 3589
  • ECONOMIC EVALUATION OF CHELATION REGIMENS FOR ?--THALASSEMIA MAJOR: A SYSTEMATIC REVIEW

    Jialian Li
    e2019036
    2019-06-24
    https://doi.org/10.4084/mjhid.2019.036
    2002
    PDF: 1453
    HTML: 228
  • CLINICAL AND BIOCHEMICAL DATA OF ADULT THALASSEMIA MAJOR PATIENTS (TM) WITH MULTIPLE ENDOCRINE COMPLICATIONS (MEC) VERSUS TM PATIENTS WITH NORMAL ENDOCRINE FUNCTIONS: A RETROSPECTIVE LONG-TERM STUDY (40 YEARS) IN A TERTIARY CARE CENTER IN ITALY

    Vincenzo De Sanctis, Heba Elsedfy
    e2016022
    2016-04-12
    https://doi.org/10.4084/mjhid.2016.022
    3785
    PDF: 1030
    HTML: 3494
  • THE ROLE OF THE CAROTID DOPPLER EXAMINATION IN THE EVALUATION OF ATHEROSCLEROTIC CHANGES IN BETA THALASSEMIA PATIENTS

    Gehan Lotfy Abdel Hakeem, hoda Abdel kereem Abdel Samei, Ashraf mohamed El Shereif, Ahlam mohamed ismail
    e2015023
    2015-02-17
    https://doi.org/10.4084/mjhid.2015.023
    2186
    PDF: 985
    HTML: 3004
    Untitled: 210
  • LONGITUDINAL STUDY ON LIVER FUNCTIONS IN PATIENTS WITH THALASSEMIA MAJOR BEFORE AND AFTER DEFERASIROX (DFX) THERAPY

    Ashraf Tawfik Soliman, Mohamed Yassin, Fawzia AlYafei, Lolwa Al-Naimi, Noora Almarri, Aml Sabt, Vincenzo De Sanctis
    e2014025
    2014-04-06
    https://doi.org/10.4084/mjhid.2014.025
    2258
    PDF: 2158
    HTML: 2437
  • JADENU® SUBSTITUTING EXJADE® IN IRON OVERLOADED ?- THALASSEMIA MAJOR (BTM) PATIENTS: A PRELIMINARY REPORT OF THE EFFECTS ON THE TOLERABILITY, SERUM FERRITIN LEVEL, LIVER IRON CONCENTRATION AND BIOCHEMICAL PROFILES

    Vincenzo De Sanctis
    e2018064
    2018-10-27
    https://doi.org/10.4084/mjhid.2018.064
    2649
    PDF: 1219
    HTML: 263
  • SEVERE LIVER IRON CONCENTRATIONS (LIC) IN 24 PATIENTS WITH ?-THALASSEMIA MAJOR: CORRELATIONS WITH SERUM FERRITIN, LIVER ENZYMES AND ENDOCRINE COMPLICATIONS

    Vincenzo De Sanctis
    e2018062
    2018-10-27
    https://doi.org/10.4084/mjhid.2018.062
    2652
    PDF: 1379
    HTML: 307
  • A A RETROSPECTIVE LONG-TERM STUDY ON AGE AT MENARCHE AND MENSTRUAL CHARACTERISTICS IN 85 YOUNG WOMEN WITH TRANSFUSION-DEPENDENT Β-THALASSEMIA (TDT) BORN BETWEEN 1965 AND 1995 Long-Term Study on Age at Menarche and Menstrual Characteristics in patients with TDT

    Vincenzo De Sanctis, Salvatore Di Maio
    e2021040
    2021-06-28
    https://doi.org/10.4084/MJHID.2021.040
    1528
    PDF: 500
    HTML: 181
  • The COST-UTILITY ANALYSIS OF FOUR CHELATION REGIMENS FOR ?-THALASSEMIA MAJOR: A CHINESE PERSPECTIVE

    Jialian Li
    e2020029
    2020-04-27
    https://doi.org/10.4084/mjhid.2020.029
    1782
    PDF: 976
    HTML: 278
  • GROWTH AND ENDOCRINE FUNCTION IN TUNISIAN THALASSEMIA MAJOR PATIENTS

    Naouel GUIRAT
    e2018031
    2018-05-01
    https://doi.org/10.4084/mjhid.2018.031
    2778
    PDF: 1018
    HTML: 422
    TABLE: 192
    FIGURES: 255
  • IRON CHELATION THERAPY WITH DEFERASIROX IN THE MANAGEMENT OF IRON OVERLOAD IN PRIMARY MYELOFIBROSIS

    Elena Maria Elli, Angelo Belotti, Andrea Aroldi, Matteo Parma, Pietro Pioltelli, Enrico Maria Pogliani
    e2014042
    2014-05-30
    https://doi.org/10.4084/mjhid.2014.042
    2134
    PDF: 1156
    HTML: 2009
  • THALASSAEMIA INTERMEDIA : AN UPDATE

    Ali Taher, Khaled M. Musallam, Maria Domenica Cappellini
    e2009004
    2009-08-17
    1069
    PDF: 441
    HTML: 9445
  • Should every patient with MDS get iron chelation – probably yes.

    Kanjaksha Ghosh, Emanuele Angelucci, Federica Pilo, Kinjalka Ghosh
    e2017055
    2017-09-01
    https://doi.org/10.4084/mjhid.2017.055
    2340
    PDF: 949
    HTML: 379
  • CONCISE REVIEW ON THE FREQUENCY, MAJOR RISK FACTORS AND SURVEILLANCE OF HEPATOCELLULAR CARCINOMA (HCC) IN ?-THALASSEMIAS: PAST, PRESENT AND FUTURE PERSPECTIVES Thalassaemia transfusion dependent, Hepatitis C, hepatocarcinoma.

    Vincenzo De Sanctis
    e2020006
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.006
    4287
    PDF: 1525
    HTML: 457
  • THALASSAEMIA AND ABERRATIONS OF GROWTH AND PUBERTY

    Andreas Kyriakou, Nicos Skordis
    e2009003
    2009-07-28
    1139
    PDF: 464
    HTML: 3220
  • A MULTICENTER ICET-A STUDY ON AGE AT MENARCHE AND MENSTRUAL CYCLES IN PATIENTS WITH TRANSFUSION-DEPENDENT THALASSEMIA (TDT) WHO STARTED EARLY CHELATION THERAPY WITH DIFFERENT CHELATING AGENTS. Age at menarche and menstrual cycles in patients with transfusion-dependent thalassemia.

    SALVATORE DI MAIO, VINCENZO DE SANCTIS, PIERLUIGI MARZUILLO, CHRISTOS KATTAMIS, SHAHINA DAAR, MEHERAN KARIMI, SAKI FOROUGH, ATANAS BANKEV, VALERIA KALEVA, SOTEROULA CHRISTOU, CARMELO FORTUGNO, POLYXENI DELAPORTA, ASHRAF T SOLIMAN , PLOUTARCHOS TZOULIS
    e2023058
    2023-10-30
    https://doi.org/10.4084/MJHID.2023.058
    793
    PDF: 511
    HTML: 116
  • THE DIAGNOSTIC VALUE OF PULSED WAVE TISSUE DOPPLER IMAGING IN ASYMPTOMATIC BETA- THALASSEMIA MAJOR CHILDREN AND YOUNG ADULTS ; RELATION TO CHEMICAL BIOMARKERS OF LEFT VENTRICULAR FUNCTION AND IRON OVERLOAD .

    Seham Ragab
    e2015051
    2015-08-24
    https://doi.org/10.4084/mjhid.2015.051
    1395
    PDF: 872
    HTML: 1362
    Untitled: 191
  • THE FREQUENCY OF ADRENAL INSUFFICIENCY IN ADOLESCENTS AND YOUNG ADULTS WITH THALASSEMIA MAJOR VERSUS THALASSEMIA INTERMEDIA IN IRAN

    Sara Matin, Masoud Ghanei Jahromi, Zohreh Karemizadeh, Sezaneh Haghpanah, Vincenzo De Sanctis, Ashraf Soliman, Mehran Karimi
    e2015005
    2014-08-28
    https://doi.org/10.4084/mjhid.2015.005
    2031
    PDF: 1077
    HTML: 9549
  • HEALTH-RELATED QUALITY OF LIFE IN THAI CHILDREN WITH THALASSEMIA AS EVALUATED BY PEDSQL AND EQ-5D-Y: A SINGLE CENTER EXPERIENCE

    Pacharapan Surapolchai, Phakatip Sinlapamongkolkul
    e2020036
    2020-06-28
    https://doi.org/10.4084/mjhid.2020.036
    1524
    PDF: 1131
    HTML: 314
  • FASTING PLASMA GLUCOSE LEVELS WITHIN THE HIGH NORMAL RANGE ARE ASSOCIATED WITH A SIGNIFICANTLY INCREASED RISK OF FUTURE DYSGLYCEMIA IN TRANSFUSION-DEPENDENT Β THALASSEMIA: A DECADE-LONG MULTICENTER RETROSPECTIVE ANALYSIS Higher normal fasting plasma glucose and glucose dysregulation in β- thalassemia

    Vincenzo De Sanctis, Forough Saki, Mehran Karimi, Mohammad Faranoush, Ihab Elhakim, Ashraf T Soliman, Shahina Daar, Ploutarchos Tzoulis
    e2025072
    2025-10-31
    https://doi.org/10.4084/MJHID.2025.072
    650
    PDF: 249
    Html: 33
  • THE PERFORMANCE OF HOMA 2 COMPARED TO DYNAMIC MARKERS OF INSULIN SECRETION AND SENSITIVITY/RESISTANCE FOR PREDICTING DYSGLYCEMIA IN TRANSFUSION-DEPENDENT Β-THALASSEMIA: THE EXPERIENCE OF A SINGLE CENTRE HOMA 2 and DYNAMIC MARKERS OF INSULIN SECRETION FOR PREDICTING DYSGLYCEMIA  in TDT

    Vincenzo De Sanctis, Shahina Daar, Ploutarchos Tzoulis, Ashraf Soliman, Ihab Elhakim , Mohammad Faranoush, Christos Kattamis
    e2026055
    2026-06-30
    https://doi.org/10.4084/MJHID.2026.056
    45
    PDF: 33
    HTML: 5
  • GLUCOSE METABOLISM AND INSULIN RESPONSE TO ORAL GLUCOSE TOLERANCE TEST (OGTT) IN PREPUBERTAL PATIENTS WITH TRANSFUSION DEPENDENT Β-THALASSEMIA (TDT): A LONG-TERM RETROSPECTIVE ANALYSIS Long-term retrospective analysis of glucose homeostasis in children with transfusion dependent β-thalassemia

    Vincenzo De Sanctis, Ashraf Soliman, Ploutarchos Tzoulis, Shahina Daar, Salvatore Di Maio, Bernadette Fiscina, Christos Kattamis
    e2021051
    2021-08-28
    https://doi.org/10.4084/MJHID.2021.051
    1732
    PDF: 548
    HTML: 167
  • Does splenectomy influence the development of Hypothyroidism in Transfusion Dependent Thalassemia Patients? A retrospective study. Splenectomy in Hypothyroidism of TDT patients

    Christos KATTAMIS, Myrto Skafida, Christalena Sofocleous, Antonis Kattamis
    e2019064
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.064
    1240
    PDF: 964
    HTML: 310
  • BETA THALASSEMIA MAJOR IN A DEVELOPING COUNTRY: EPIDEMIOLOGICAL, CLINICAL AND EVOLUTIONARY ASPECT

    Mohamed Bejaoui, Naouel Guirat
    e2013002
    2013-01-01
    https://doi.org/10.4084/mjhid.2013.002
    1623
    PDF: 905
    HTML: 2510
  • INFECTIONS IN THALASSEMIA AND HEMOGLOBINOPATHIES

    Bianca Maria Ricerca, Arturo Di Girolamo, Deborah Rund
    e2009028
    2009-12-28
    1090
    PDF: 614
    HTML: 4407
  • NEW TREATMENTS FOR MYELODYSPLASTIC SYNDROMES

    Francesco D'Alò, Mariangela Greco, Marianna Criscuolo, Maria Teresa Voso
    e2010021
    2010-08-11
    https://doi.org/10.4084/mjhid.2010.021
    1982
    PDF: 758
    HTML: 702
  • STUDY OF SERUM HAPTOGLOBIN LEVEL AND ITS RELATION TO ERYTHROPOIETIC ACTIVITY IN BETA THALASSEMIA CHILDREN .

    Seham Ragab, Manal A. Safan, Eman A. Badr
    e2015019
    2015-02-12
    https://doi.org/10.4084/mjhid.2015.019
    2208
    PDF: 1174
    HTML: 2591
    Study of serum haptoglobin level in thalassemia: 348
    Figures: 178
  • FIRST-PHASE INSULIN RESPONSE (FPIR) TO INTRAVENOUS GLUCOSE TOLERANCE TEST (IVGTT), INSULIN SENSITIVITY AND LONG-TERM FOLLOW-UP IN TRANSFUSION-DEPENDENT BETA-THALASSEMIA (TDT) NORMOGLYCEMIC PATIENTS WITH REDUCED INSULIN SECRETION TO ORAL GLUCOSE TOLERANCE TEST: A PILOT STUDY. The function of the endocrine pancreas in transfusion-dependent ?-thalassemia

    Vincenzo De Sanctis
    e2021021
    2021-02-26
    https://doi.org/10.4084/mjhid.2021.021
    7363
    PDF: 562
    HTML: 236
  • LONG-TERM EFFECTIVENESS, SAFETY, AND TOLERABILITY OF TWICE-DAILY DOSING WITH DEFERASIROX IN CHILDREN WITH TRANSFUSION-DEPENDENT THALASSEMIAS UNRESPONSIVE TO STANDARD ONCE-DAILY DOSING

    Jassada Buaboonnam, Chayamon Takpradit, Vip Viprakasit, Nattee Narkbunnam, Nassawee Vathana, Kamon Phuakpet, Kleebsabai Sanpakit, Bunchoo Pongtanakul
    e2021065
    2021-10-29
    https://doi.org/10.4084/MJHID.2021.065
    1171
    PDF: 428
    HTML: 165
  • DOES INSULIN LIKE GROWTH FACTOR-1 (IGF-1) DEFICIENCY HAVE A “PROTECTIVE” ROLE IN THE DEVELOPMENT OF DIABETIC RETINOPATHY IN THALASSEMIA MAJOR PATIENTS?

    Vincenzo De Sanctis
    e2015038
    2015-05-20
    https://doi.org/10.4084/mjhid.2015.038
    1974
    PDF: 935
    HTML: 5066
  • REVIEW AND RECOMMENDATIONS ON MANAGEMENT OF ADULT FEMALE THALASSEMIA PATIE?TS WITH HYPOGONADISM BASED ON LITERATURE REVIEW AND EXPERIENCE OF ICET-A NETWORK SPECIALISTS

    Vincenzo De Sanctis
    e2017001
    2017-01-01
    https://doi.org/10.4084/mjhid.2017.001
    6141
    PDF: 1438
    HTML: 1939
  • INSULIN-LIKE GROWTH FACTOR-1 (IGF-1): DEMOGRAPHIC, CLINICAL AND LABORATORY DATA IN 120 CONSECUTIVE ADULT PATIENTS WITH THALASSAEMIA MAJOR

    V. De Sanctis
    e2014.074
    2014-11-01
    https://doi.org/10.4084/mjhid.2014.074
    2261
    PDF: 948
    HTML: 26946
  • POST-LOAD PLASMA GLUCOSE INCREASE (PG-GAP) AS A RISK FACTOR FOR DEVELOPING DYSGLYCEMIA IN PATIENTS WITH TRANSFUSION-DEPENDENT Β-THALASSEMIA (Β-TDT): RETROSPECTIVE ANALYSIS OVER 8 YEARS Post load plasma glucose increase and the risk of glucose dysregulation in thalassemia

    Vincenzo De Sanctis, Mohammad Faranoush, Efthymia Vlachaki, Theodora- Maria Venou, Ashraf T Soliman, Shahina Daar, Ploutarchos Tzoulis, Christos Kattamis
    e2025069
    2025-10-31
    https://doi.org/10.4084/MJHID.2025.069
    511
    PDF: 249
    HTML: 43
  • COULD PLASMA GLUCOSE (PG) INCREMENT (PG %) EXPAND THE CLINICAL WEIGHT OF OGTT? PRELIMINARY FINDINGS IN 19 TDT PATIENTS (Β-TDT) WITH NORMAL GLUCOSE TOLERANCE Plasma glucose (PG) increment (PG %) and pancretic β-cell dysfunction in thalassemia

    Vincenzo De Sanctis, Ashraf Soliman, Shahina Daar, Ploutarchos Tzoulis, Christos Kattamis
    e2025050
    2025-06-29
    https://doi.org/10.4084/MJHID.2025.050
    733
    PDF: 509
    HTML: 49
  • A MULTICENTER ICET-A SURVEY ON ADHERENCE TO ANNUAL ORAL GLUCOSE TOLERANCE TEST (OGTT) SCREENING IN TRANSFUSION-DEPENDENT THALASSEMIA (TDT) PATIENTS - THE EXPERT CLINICIANS’ OPINION ON FACTORS INFLUENCING THE ADHERENCE AND ON ALTERNATIVE STRATEGIES FOR ADHERENCE OPTIMIZATION Survey on adherence to annual OGTT in thalassemia

    Vincenzo De Sanctis
    e2025008
    2024-12-31
    https://doi.org/10.4084/MJHID.2025.008
    2930
    PDF: 1346
    HTML: 159
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