A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β⁺-Thalassaemia Patient

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Marta Bortolotti
Gianluca Costamagna
Marta Mancarella
Delia Gagliardi
Silvia Lanfranconi
Alessia Marcon
Margherita Migone De Amicis
Nereo Bresolin
Stefania Corti
Giovanna Graziadei


sickle cell disease, cerebral fat embolism, status epilepticus, eritroexchange


Sickle cell disease (SCD) refers to a group of hereditary disorders associated with clinical manifestations of variable severity. C In particular, Fat Embolism Syndrome, a rare and devastating complication of SCD, may preferentially involve non-homozygous patients and patients with mild disease. 


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