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Editor-in-Chief: Giuseppe Leone | Italy

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  • DEFERASIROX: OVER A DECADE OF EXPERIENCE IN THALASSEMIA

    Ali Taher
    e2018066
    2018-11-01
    https://doi.org/10.4084/mjhid.2018.066
    2871
    PDF: 1575
    HTML: 224
  • IRON CHELATION THERAPY IN THALASSEMIA SYNDROMES

    Paolo Cianciulli
    e2009034
    1231
    PDF: 610
    HTML: 2310
  • MYELODYSPLASTIC SYNDROMES AND IRON CHELATION THERAPY

    Emanuele Angelucci, Silvana Anna Maria Urru, Federica Pilo, Alberto Piperno
    e2017021
    2017-03-01
    https://doi.org/10.4084/mjhid.2017.021
    3342
    PDF: 1284
    HTML: 1854
    Fig.1: 195
    Fig. 2: 198
  • LONG-TERM EFFECTIVENESS, SAFETY, AND TOLERABILITY OF TWICE-DAILY DOSING WITH DEFERASIROX IN CHILDREN WITH TRANSFUSION-DEPENDENT THALASSEMIAS UNRESPONSIVE TO STANDARD ONCE-DAILY DOSING

    Jassada Buaboonnam, Chayamon Takpradit, Vip Viprakasit, Nattee Narkbunnam, Nassawee Vathana, Kamon Phuakpet, Kleebsabai Sanpakit, Bunchoo Pongtanakul
    e2021065
    2021-10-29
    https://doi.org/10.4084/MJHID.2021.065
    1109
    PDF: 410
    HTML: 153
  • TRANSIENT ELASTOGRAPHY (TE) IS A USEFUL TOOL FOR ASSESSING THE RESPONSE OF LIVER IRON CHELATION IN SICKLE CELL DISEASE PATIENTS

    SOPHIA DELICOU
    e2018049
    2018-09-01
    https://doi.org/10.4084/mjhid.2018.049
    1504
    PDF: 798
    HTML: 182
  • IRON CHELATION THERAPY WITH DEFERASIROX IN THE MANAGEMENT OF IRON OVERLOAD IN PRIMARY MYELOFIBROSIS

    Elena Maria Elli, Angelo Belotti, Andrea Aroldi, Matteo Parma, Pietro Pioltelli, Enrico Maria Pogliani
    e2014042
    2014-05-30
    https://doi.org/10.4084/mjhid.2014.042
    2089
    PDF: 1137
    HTML: 1983
  • THERAPEUTIC VALUE OF COMBINED THERAPY WITH DEFERASIROX AND SILYMARIN ON IRON OVERLOAD IN CHILDREN WITH BETA THALASSEMIA

    adel abd elhaleim hagag
    e2013065
    2013-11-04
    https://doi.org/10.4084/mjhid.2013.065
    2552
    PDF: 820
    HTML: 14935
    Therapeutic Value of Combined Therapy with Deferasirox and Silymarin on Iron Overload in Children with Beta Thalassemia: 293
  • A Young Adult with Unintentional Acute Parenteral Iron intoxication Treated with Oral Chelation: The Use of Liver Ferriscan.

    Vincenzo De Sanctis
    e2017008
    2017-01-01
    https://doi.org/10.4084/mjhid.2017.008
    3074
    PDF: 999
    HTML: 1641
  • ECONOMIC EVALUATION OF CHELATION REGIMENS FOR ?--THALASSEMIA MAJOR: A SYSTEMATIC REVIEW

    Jialian Li
    e2019036
    2019-06-24
    https://doi.org/10.4084/mjhid.2019.036
    1960
    PDF: 1434
    HTML: 219
  • JADENU® SUBSTITUTING EXJADE® IN IRON OVERLOADED ?- THALASSEMIA MAJOR (BTM) PATIENTS: A PRELIMINARY REPORT OF THE EFFECTS ON THE TOLERABILITY, SERUM FERRITIN LEVEL, LIVER IRON CONCENTRATION AND BIOCHEMICAL PROFILES

    Vincenzo De Sanctis
    e2018064
    2018-10-27
    https://doi.org/10.4084/mjhid.2018.064
    2572
    PDF: 1200
    HTML: 238
  • THE HISTORY OF DEFERIPRONE (L1) AND THE COMPLETE TREATMENT OF IRON OVERLOAD IN THALASSAEMIA The history and roles of deferiprone

    George J Kontoghiorghes, Marios Kleanthous, Christina N. Kontoghiorghe
    e2020011
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.011
    2361
    PDF: 1571
    HTML: 607
  • BETA THALASSEMIA MAJOR IN A DEVELOPING COUNTRY: EPIDEMIOLOGICAL, CLINICAL AND EVOLUTIONARY ASPECT

    Mohamed Bejaoui, Naouel Guirat
    e2013002
    2013-01-01
    https://doi.org/10.4084/mjhid.2013.002
    1590
    PDF: 890
    HTML: 2470
  • LONGITUDINAL STUDY ON LIVER FUNCTIONS IN PATIENTS WITH THALASSEMIA MAJOR BEFORE AND AFTER DEFERASIROX (DFX) THERAPY

    Ashraf Tawfik Soliman, Mohamed Yassin, Fawzia AlYafei, Lolwa Al-Naimi, Noora Almarri, Aml Sabt, Vincenzo De Sanctis
    e2014025
    2014-04-06
    https://doi.org/10.4084/mjhid.2014.025
    2178
    PDF: 2131
    HTML: 2421
  • Rhino-Orbital-Cerebral Mucormycosis after Allogeneic Hematopoietic Stem Cell Transplantation and Isavuconazole Therapeutic Drug Monitoring during Intestinal Graft versus Host Disease

    Giacomo Andreani, Gianluca Fadda, Dario Gned, Matteo Dragani, Giovanni Cavallo, Valentina Monticone, Alessandro Morotti, Marco De Gobbi, Angelo Guerrasio, Antonio D'Avolio, Daniela Cilloni
    e2019061
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.061
    1369
    PDF: 1059
    HTML: 188
  • ASSOCİATİON BETWEEN IRON OVERLOAD AND GLUCOSE METABOLİSM İN CHİLDREN AND YOUTH WİTH TRANSFUSİON-DEPENDENT BETA THALASSEMİA: THE ROLE OF CHELATİON THERAPY

    Deniz Guven, Dr. İncefidan, Dr. Kazanci, Dr. Ozlem Kara
    2026-02-28
    https://doi.org/10.4084/MJHID.2026.017
    596
    PDF: 445
    HTML: 63
  • GLUCOSE HOMEOSTASIS AND ΑSSESSMENT OF Β-CELL FUNCTION BY 3-HOUR ORAL GLUCOSE TOLERANCE (OGTT) IN PATIENTS WITH Β-THALASSEMIA MAJOR WITH SERUM FERRITIN BELOW 1,000 NG/DL: RESULTS FROM A SINGLE ICET-A CENTRE OGTT in thalassemia and iron overload

    Vincenzo De Sanctis, Ashraf Soliman, Shahina Daar, Ploutarchos Tzoulis , Salvatore Di Maio, Christos Kattamis
    e2023006
    2023-01-01
    https://doi.org/10.4084/MJHID.2023.006
    3869
    PDF: 1087
    HTML: 423
  • CARDIAC FUNCTION AND IRON CHELATION IN THALASSEMIA MAJOR AND INTERMEDIA: A REVIEW OF THE UNDERLYING PATHOPHYSIOLOGY AND APPROACH TO CHELATION MANAGEMENT

    Athanasios Aessopos, Vasilios Berdoukas
    e2009002
    2009-07-18
    1560
    PDF: 479
    HTML: 1427
  • SEVERE LIVER IRON CONCENTRATIONS (LIC) IN 24 PATIENTS WITH ?-THALASSEMIA MAJOR: CORRELATIONS WITH SERUM FERRITIN, LIVER ENZYMES AND ENDOCRINE COMPLICATIONS

    Vincenzo De Sanctis
    e2018062
    2018-10-27
    https://doi.org/10.4084/mjhid.2018.062
    2501
    PDF: 1338
    HTML: 293
  • PREVENTION OF ? THALASSEMIA IN NORTHERN ISRAEL - A COST-BENEFIT ANALYSIS.

    Ariel Koren, Lora Profeta, Luci Zalman, Haya Palmor, Carina Levin, Ronit Bril Zamir, Stavit Shalev, Orna Blondheim
    e2014012
    2014-02-17
    https://doi.org/10.4084/mjhid.2014.012
    2450
    PDF: 1143
    HTML: 11789
  • The COST-UTILITY ANALYSIS OF FOUR CHELATION REGIMENS FOR ?-THALASSEMIA MAJOR: A CHINESE PERSPECTIVE

    Jialian Li
    e2020029
    2020-04-27
    https://doi.org/10.4084/mjhid.2020.029
    1704
    PDF: 958
    HTML: 265
  • NEW TREATMENTS FOR MYELODYSPLASTIC SYNDROMES

    Francesco D'Alò, Mariangela Greco, Marianna Criscuolo, Maria Teresa Voso
    e2010021
    2010-08-11
    https://doi.org/10.4084/mjhid.2010.021
    1929
    PDF: 735
    HTML: 686
  • EARLY PREDICTORS OF RENAL DYSFUNCTION IN ?-THALASSEMIA MAJOR AND INTERMEDIA PATIENTS

    Azza A.G. Tantawy, Nagham El Bablawy, Amira A. M Adly, Fatma S E Ebeid
    e2014057
    2004-09-01
    https://doi.org/10.4084/mjhid.2014.057
    1912
    PDF: 940
    HTML: 3789
  • ZYGOMYCOSIS IN IMMUNOCOMPROMISED NON-HAEMATOLOGICAL PATIENTS

    George Petrikkos, Miranda Drogari-Apiranthitou
    e2011012
    2011-03-14
    https://doi.org/10.4084/mjhid.2011.012
    2781
    PDF: 936
    HTML: 7317
  • THE DIAGNOSTIC VALUE OF PULSED WAVE TISSUE DOPPLER IMAGING IN ASYMPTOMATIC BETA- THALASSEMIA MAJOR CHILDREN AND YOUNG ADULTS ; RELATION TO CHEMICAL BIOMARKERS OF LEFT VENTRICULAR FUNCTION AND IRON OVERLOAD .

    Seham Ragab
    e2015051
    2015-08-24
    https://doi.org/10.4084/mjhid.2015.051
    1370
    PDF: 861
    HTML: 1347
    Untitled: 183
  • LIVER IRON CONTENT (LIC) IN ADULTS WITH NON-TRANSFUSION DEPENDENT SICKLE CELL DISEASE (NT-SCD). CORRELATION WITH SERUM FERRITIN AND LIVER ENZYMES CONCENTRATIONS

    Vincenzo De Sanctis
    e2017037
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.037
    3783
    PDF: 952
    HTML: 1139
  • ASSOCIATION OF VDBP RS4701 VARIANT, BUT NOT VDR/RXR-? OVER-EXPRESSION WITH BONE MINERAL DENSITY IN PEDIATRIC ?-THALASSEMIA PATIENTS Vitamin D metabolic axis and BMD in ?-thalassemia

    Shaimaa Sahmoud, Mostafa S. Ibrahim, Eman A. Toraih, Noha Kamel, Manal Fawzy, Samar Elfiky
    e2020037
    2020-06-28
    https://doi.org/10.4084/mjhid.2020.037
    1185
    PDF: 715
    HTML: 176
  • HEALTH-RELATED QUALITY OF LIFE IN THAI CHILDREN WITH THALASSEMIA AS EVALUATED BY PEDSQL AND EQ-5D-Y: A SINGLE CENTER EXPERIENCE

    Pacharapan Surapolchai, Phakatip Sinlapamongkolkul
    e2020036
    2020-06-28
    https://doi.org/10.4084/mjhid.2020.036
    1464
    PDF: 1111
    HTML: 290
  • FASTING PLASMA GLUCOSE LEVELS WITHIN THE HIGH NORMAL RANGE ARE ASSOCIATED WITH A SIGNIFICANTLY INCREASED RISK OF FUTURE DYSGLYCEMIA IN TRANSFUSION-DEPENDENT Β THALASSEMIA: A DECADE-LONG MULTICENTER RETROSPECTIVE ANALYSIS Higher normal fasting plasma glucose and glucose dysregulation in β- thalassemia

    Vincenzo De Sanctis, Forough Saki, Mehran Karimi, Mohammad Faranoush, Ihab Elhakim, Ashraf T Soliman, Shahina Daar, Ploutarchos Tzoulis
    e2025072
    2025-10-31
    https://doi.org/10.4084/MJHID.2025.072
    607
    PDF: 212
    Html: 28
  • GROWTH AND ENDOCRINE FUNCTION IN TUNISIAN THALASSEMIA MAJOR PATIENTS

    Naouel GUIRAT
    e2018031
    2018-05-01
    https://doi.org/10.4084/mjhid.2018.031
    2695
    PDF: 998
    HTML: 404
    TABLE: 182
    FIGURES: 238
  • VASCULAR ENDOTHELIAL GROWTH FACTOR IN CHILDREN WITH THALASSEMIA MAJOR PDF

    sameh samir fahmey, Hassan Naguib, sanna Abdelshafy, rasha Alashry
    e2013044
    2013-06-05
    https://doi.org/10.4084/mjhid.2013.044
    1290
    PDF: 852
    HTML: 1028
    Figure 1 the correlation between frequency of blood transfusion and serum vascular endothelial growth factor (VEGF).: 168
  • CORRELATION OF TRANSIENT ELASTOGRAPHY WITH LIVER IRON CONCENTRATION, AND SERUM FERRITIN LEVELS IN PATIENTS WITH TRANSFUSION-DEPENDENT THALASSEMIA MAJOR PATIENTS FROM OMAN

    Hammad Khan, Vinodh Panjwani, Sara Al Rahbi, Abubakr Eltigani , Rizwan Qureshi, Khaleeq Unnisa, Najmus Sehar, Alok Mittal, Anil Pathare
    e2023048
    2023-08-29
    https://doi.org/10.4084/MJHID.2023.048
    1023
    PDF: 668
    HTML: 178
  • THE ICET-A RECOMMENDATIONS FOR THE DIAGNOSIS AND MANAGEMENT OF DISTURBANCES OF GLUCOSE HOMEOSTASIS IN THALASSEMIA MAJOR PATIENTS

    Vincenzo De Sanctis
    e2016058
    2016-10-25
    https://doi.org/10.4084/mjhid.2016.058
    4174
    PDF: 1176
    HTML: 1169
  • POST-LOAD PLASMA GLUCOSE INCREASE (PG-GAP) AS A RISK FACTOR FOR DEVELOPING DYSGLYCEMIA IN PATIENTS WITH TRANSFUSION-DEPENDENT Β-THALASSEMIA (Β-TDT): RETROSPECTIVE ANALYSIS OVER 8 YEARS Post load plasma glucose increase and the risk of glucose dysregulation in thalassemia

    Vincenzo De Sanctis, Mohammad Faranoush, Efthymia Vlachaki, Theodora- Maria Venou, Ashraf T Soliman, Shahina Daar, Ploutarchos Tzoulis, Christos Kattamis
    e2025069
    2025-10-31
    https://doi.org/10.4084/MJHID.2025.069
    466
    PDF: 234
    HTML: 34
  • Luspatercept Treatment in a β-Thalassemia Patient with Pulmonary Arterial Hypertension: A Case Report

    beibei yang, dongmei liu, changyu yang, Yali zhou, Guiping Liao, jian huang, Yingying Li, yinjiang tang, xiaolin yin
    e2025059
    2025-08-31
    https://doi.org/10.4084/MJHID.2025.059
    999
    PDF: 528
    Html: 135
  • DOES INSULIN LIKE GROWTH FACTOR-1 (IGF-1) DEFICIENCY HAVE A “PROTECTIVE” ROLE IN THE DEVELOPMENT OF DIABETIC RETINOPATHY IN THALASSEMIA MAJOR PATIENTS?

    Vincenzo De Sanctis
    e2015038
    2015-05-20
    https://doi.org/10.4084/mjhid.2015.038
    1917
    PDF: 921
    HTML: 5052
  • Does splenectomy influence the development of Hypothyroidism in Transfusion Dependent Thalassemia Patients? A retrospective study. Splenectomy in Hypothyroidism of TDT patients

    Christos KATTAMIS, Myrto Skafida, Christalena Sofocleous, Antonis Kattamis
    e2019064
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.064
    1190
    PDF: 918
    HTML: 300
  • INFECTIONS IN MYELODYSPLASTIC SYNDROME IN RELATION TO STAGE AND THERAPY

    Giuseppe Leone, Livio Pagano
    e2018039
    2018-07-01
    https://doi.org/10.4084/mjhid.2018.039
    4124
    PDF: 1443
    HTML: 586
  • STUDY OF SERUM HAPTOGLOBIN LEVEL AND ITS RELATION TO ERYTHROPOIETIC ACTIVITY IN BETA THALASSEMIA CHILDREN .

    Seham Ragab, Manal A. Safan, Eman A. Badr
    e2015019
    2015-02-12
    https://doi.org/10.4084/mjhid.2015.019
    2154
    PDF: 1160
    HTML: 2576
    Study of serum haptoglobin level in thalassemia: 339
    Figures: 172
  • A MULTICENTER ICET-A STUDY ON AGE AT MENARCHE AND MENSTRUAL CYCLES IN PATIENTS WITH TRANSFUSION-DEPENDENT THALASSEMIA (TDT) WHO STARTED EARLY CHELATION THERAPY WITH DIFFERENT CHELATING AGENTS. Age at menarche and menstrual cycles in patients with transfusion-dependent thalassemia.

    SALVATORE DI MAIO, VINCENZO DE SANCTIS, PIERLUIGI MARZUILLO, CHRISTOS KATTAMIS, SHAHINA DAAR, MEHERAN KARIMI, SAKI FOROUGH, ATANAS BANKEV, VALERIA KALEVA, SOTEROULA CHRISTOU, CARMELO FORTUGNO, POLYXENI DELAPORTA, ASHRAF T SOLIMAN , PLOUTARCHOS TZOULIS
    e2023058
    2023-10-30
    https://doi.org/10.4084/MJHID.2023.058
    749
    PDF: 489
    HTML: 102
  • BACTERIAL INFECTIONS FOLLOWING SPLENECTOMY FOR MALIGNANT AND NONMALIGNANT HEMATOLOGIC DISEASES

    Giuseppe Leone, Eligio Pizzigallo
    e2015057
    2015-10-12
    https://doi.org/10.4084/mjhid.2015.057
    4810
    PDF: 1953
    HTML: 8302
  • BONE MINERAL DENSITY AND VITAMIN D RECEPTOR GENETIC VARIANTS IN EGYPTIAN CHILDREN WITH BETA THALASSEMIA ON VITAMIN D SUPPLEMENTATION

    Hadeer A Abbassy, Reham Abdel Haleem Abo Elwafa, Omneya Magdy Omar
    e2019013
    2019-01-01
    https://doi.org/10.4084/mjhid.2019.013
    2225
    PDF: 1214
    HTML: 204
  • CONCISE REVIEW ON THE FREQUENCY, MAJOR RISK FACTORS AND SURVEILLANCE OF HEPATOCELLULAR CARCINOMA (HCC) IN ?-THALASSEMIAS: PAST, PRESENT AND FUTURE PERSPECTIVES Thalassaemia transfusion dependent, Hepatitis C, hepatocarcinoma.

    Vincenzo De Sanctis
    e2020006
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.006
    4198
    PDF: 1510
    HTML: 440
  • INSULIN-LIKE GROWTH FACTOR-1 (IGF-1): DEMOGRAPHIC, CLINICAL AND LABORATORY DATA IN 120 CONSECUTIVE ADULT PATIENTS WITH THALASSAEMIA MAJOR

    V. De Sanctis
    e2014.074
    2014-11-01
    https://doi.org/10.4084/mjhid.2014.074
    2220
    PDF: 929
    HTML: 26932
  • Should every patient with MDS get iron chelation – probably yes.

    Kanjaksha Ghosh, Emanuele Angelucci, Federica Pilo, Kinjalka Ghosh
    e2017055
    2017-09-01
    https://doi.org/10.4084/mjhid.2017.055
    2281
    PDF: 940
    HTML: 366
  • HEMATOPOIETIC STEM CELL TRNSPLANTATION IN THALASSEMIA AND RELATED DISORDERS

    Emanuele Angelucci, Federica Pilo, Clara Targhetta, Martina Pettinau, Cristina Depau, Claudia Cogoni, Sara Usai, Mario Pani, Laura Dessì, Donatella Baronciani
    e2009015
    1387
    PDF: 487
    HTML: 3951
  • A A RETROSPECTIVE LONG-TERM STUDY ON AGE AT MENARCHE AND MENSTRUAL CHARACTERISTICS IN 85 YOUNG WOMEN WITH TRANSFUSION-DEPENDENT Β-THALASSEMIA (TDT) BORN BETWEEN 1965 AND 1995 Long-Term Study on Age at Menarche and Menstrual Characteristics in patients with TDT

    Vincenzo De Sanctis, Salvatore Di Maio
    e2021040
    2021-06-28
    https://doi.org/10.4084/MJHID.2021.040
    1468
    PDF: 487
    HTML: 170
  • Late-onset male hypogonadism and fertility potential in thalassemia major patients: Two emerging issues

    Vincenzo De Sanctis
    e2015047
    2015-07-08
    https://doi.org/10.4084/mjhid.2015.047
    1759
    PDF: 924
    HTML: 778
  • AGING WITH THALASSEMIA AND SICKLE CELL DISEASE: A GERONTOLOGICAL MODEL OF ACCELERATED MULTIMORBIDITY AND FUNCTION-CENTERED CARE BEYOND MIDLIFE Thalassemia and Sickle Cell Diseases: Effect of Aging

    Dr.Sophia Delicou, Dr.Ioannis Ilias, Dr.Athanasia Kapota, Dr.Elena Papatheodorou, Dr.Maria Moraki, Dr.Aikaterini Xydaki, Dr.Alexandra Mika, Dr.Panagiota Giannou, Dr.Irene Kouroukli, Dr.Theodoros Aforozis, Dr.Myrto Palkopoulou, Dr.Christos Savvidis, Dr.Iliana Mani, Prof.Constantina Aggeli, Prof. John Koskinas
    e2026039
    2026-04-30
    https://doi.org/10.4084/MJHID.2026.039
    251
    PDF: 195
    Suppl. Files: 36
    HTML: 7
  • DIAMOND BLACKFAN ANEMIA: A TERTIARY CARE CENTRE EXPERIENCE

    avinash kumar singh, tulika seth, nita radhakrishnan, pravas mishra, manoranjan mahapatra, haraprasad pati
    e2013039
    2013-06-03
    https://doi.org/10.4084/mjhid.2013.039
    1783
    PDF: 848
    HTML: 3588
    Diamond Blackfan Anemia: A Tertiary care centre experience: 249
  • HEMOGLOBIN H DISEASE AND GROWTH: A COMPARATIVE STUDY OF DHbH AND NDHbH PATIENTS

    Issanun Hunnuan, Kleebsabai SAnpakit, Ornsuda Lertbannaphong, Jassada Buaboonnam
    e2023045
    2023-08-29
    https://doi.org/10.4084/MJHID.2023.045
    1220
    PDF: 645
    HTML: 156
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