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Editor-in-Chief: Giuseppe Leone | Italy

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  • THE HISTORY OF DEFERIPRONE (L1) AND THE COMPLETE TREATMENT OF IRON OVERLOAD IN THALASSAEMIA The history and roles of deferiprone

    George J Kontoghiorghes, Marios Kleanthous, Christina N. Kontoghiorghe
    e2020011
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.011
    2437
    PDF: 1601
    HTML: 649
  • IRON CHELATION THERAPY IN THALASSEMIA SYNDROMES

    Paolo Cianciulli
    e2009034
    1280
    PDF: 619
    HTML: 2323
  • CARDIAC FUNCTION AND IRON CHELATION IN THALASSEMIA MAJOR AND INTERMEDIA: A REVIEW OF THE UNDERLYING PATHOPHYSIOLOGY AND APPROACH TO CHELATION MANAGEMENT

    Athanasios Aessopos, Vasilios Berdoukas
    e2009002
    2009-07-18
    1600
    PDF: 488
    HTML: 1447
  • ECONOMIC EVALUATION OF CHELATION REGIMENS FOR ?--THALASSEMIA MAJOR: A SYSTEMATIC REVIEW

    Jialian Li
    e2019036
    2019-06-24
    https://doi.org/10.4084/mjhid.2019.036
    2017
    PDF: 1458
    HTML: 231
  • DEFERASIROX: OVER A DECADE OF EXPERIENCE IN THALASSEMIA

    Ali Taher
    e2018066
    2018-11-01
    https://doi.org/10.4084/mjhid.2018.066
    2955
    PDF: 1601
    HTML: 239
  • The COST-UTILITY ANALYSIS OF FOUR CHELATION REGIMENS FOR ?-THALASSEMIA MAJOR: A CHINESE PERSPECTIVE

    Jialian Li
    e2020029
    2020-04-27
    https://doi.org/10.4084/mjhid.2020.029
    1813
    PDF: 979
    HTML: 280
  • THE ICET-A RECOMMENDATIONS FOR THE DIAGNOSIS AND MANAGEMENT OF DISTURBANCES OF GLUCOSE HOMEOSTASIS IN THALASSEMIA MAJOR PATIENTS

    Vincenzo De Sanctis
    e2016058
    2016-10-25
    https://doi.org/10.4084/mjhid.2016.058
    4257
    PDF: 1222
    HTML: 1209
  • DOES INSULIN LIKE GROWTH FACTOR-1 (IGF-1) DEFICIENCY HAVE A “PROTECTIVE” ROLE IN THE DEVELOPMENT OF DIABETIC RETINOPATHY IN THALASSEMIA MAJOR PATIENTS?

    Vincenzo De Sanctis
    e2015038
    2015-05-20
    https://doi.org/10.4084/mjhid.2015.038
    1993
    PDF: 941
    HTML: 5067
  • BETA THALASSEMIA MAJOR IN A DEVELOPING COUNTRY: EPIDEMIOLOGICAL, CLINICAL AND EVOLUTIONARY ASPECT

    Mohamed Bejaoui, Naouel Guirat
    e2013002
    2013-01-01
    https://doi.org/10.4084/mjhid.2013.002
    1636
    PDF: 908
    HTML: 2514
  • A Young Adult with Unintentional Acute Parenteral Iron intoxication Treated with Oral Chelation: The Use of Liver Ferriscan.

    Vincenzo De Sanctis
    e2017008
    2017-01-01
    https://doi.org/10.4084/mjhid.2017.008
    3146
    PDF: 1028
    HTML: 1656
  • GLUCOSE HOMEOSTASIS AND ΑSSESSMENT OF Β-CELL FUNCTION BY 3-HOUR ORAL GLUCOSE TOLERANCE (OGTT) IN PATIENTS WITH Β-THALASSEMIA MAJOR WITH SERUM FERRITIN BELOW 1,000 NG/DL: RESULTS FROM A SINGLE ICET-A CENTRE OGTT in thalassemia and iron overload

    Vincenzo De Sanctis, Ashraf Soliman, Shahina Daar, Ploutarchos Tzoulis , Salvatore Di Maio, Christos Kattamis
    e2023006
    2023-01-01
    https://doi.org/10.4084/MJHID.2023.006
    3969
    PDF: 1125
    HTML: 460
  • PREVENTION OF ? THALASSEMIA IN NORTHERN ISRAEL - A COST-BENEFIT ANALYSIS.

    Ariel Koren, Lora Profeta, Luci Zalman, Haya Palmor, Carina Levin, Ronit Bril Zamir, Stavit Shalev, Orna Blondheim
    e2014012
    2014-02-17
    https://doi.org/10.4084/mjhid.2014.012
    2579
    PDF: 1220
    HTML: 11809
  • GROWTH AND ENDOCRINE FUNCTION IN TUNISIAN THALASSEMIA MAJOR PATIENTS

    Naouel GUIRAT
    e2018031
    2018-05-01
    https://doi.org/10.4084/mjhid.2018.031
    2808
    PDF: 1029
    HTML: 423
    TABLE: 195
    FIGURES: 260
  • JADENU® SUBSTITUTING EXJADE® IN IRON OVERLOADED ?- THALASSEMIA MAJOR (BTM) PATIENTS: A PRELIMINARY REPORT OF THE EFFECTS ON THE TOLERABILITY, SERUM FERRITIN LEVEL, LIVER IRON CONCENTRATION AND BIOCHEMICAL PROFILES

    Vincenzo De Sanctis
    e2018064
    2018-10-27
    https://doi.org/10.4084/mjhid.2018.064
    2658
    PDF: 1221
    HTML: 264
  • FASTING PLASMA GLUCOSE LEVELS WITHIN THE HIGH NORMAL RANGE ARE ASSOCIATED WITH A SIGNIFICANTLY INCREASED RISK OF FUTURE DYSGLYCEMIA IN TRANSFUSION-DEPENDENT Β THALASSEMIA: A DECADE-LONG MULTICENTER RETROSPECTIVE ANALYSIS Higher normal fasting plasma glucose and glucose dysregulation in β- thalassemia

    Vincenzo De Sanctis, Forough Saki, Mehran Karimi, Mohammad Faranoush, Ihab Elhakim, Ashraf T Soliman, Shahina Daar, Ploutarchos Tzoulis
    e2025072
    2025-10-31
    https://doi.org/10.4084/MJHID.2025.072
    672
    PDF: 254
    Html: 33
  • EARLY PREDICTORS OF RENAL DYSFUNCTION IN ?-THALASSEMIA MAJOR AND INTERMEDIA PATIENTS

    Azza A.G. Tantawy, Nagham El Bablawy, Amira A. M Adly, Fatma S E Ebeid
    e2014057
    2004-09-01
    https://doi.org/10.4084/mjhid.2014.057
    1978
    PDF: 954
    HTML: 3809
  • ZYGOMYCOSIS IN IMMUNOCOMPROMISED NON-HAEMATOLOGICAL PATIENTS

    George Petrikkos, Miranda Drogari-Apiranthitou
    e2011012
    2011-03-14
    https://doi.org/10.4084/mjhid.2011.012
    2870
    PDF: 964
    HTML: 7350
  • High Prevalence of Antiphospholipid Antibodies in Children with Non-Transfusion Dependent Thalassemia and Possible Correlations with Microparticles Antiphospholipid Antibodies and Thalassemia in children

    Jitlada Chinsuwan, Phatchanat Klaihmon, Praguywan Kadegasem, Ampaiwan Chuansumrit, Anucha Soisamrong, Kovit Pattanapanyasat, Pakawan Wongwerawattanakoon, Nongnuch Sirachainan
    e2020071
    2020-10-27
    https://doi.org/10.4084/mjhid.2020.071
    964
    PDF: 612
    HTML: 290
  • PREDISPOSING FACTORS TO INFECTIONS IN THALASSEMIA SYNDROME PATIENTS

    Eman M Mansory, Lina M. Abdulrahman, Balsam Osman, Sawsan M. Sawsan, Assil F. Ruckn, Marwa Aljedaani, Nemmat Hassan, Ahmed S. Barefah, Hatem M. Alahwal, Yassir Daghistani, Salem M. Bahashwan, Abdullah T. Almohammadi, Osman O. Radhwi
    e2025055
    2025-08-31
    https://doi.org/10.4084/MJHID.2025.055
    1766
    PDF: 1476
    HTML: 359
  • HEALTH-RELATED QUALITY OF LIFE IN THAI CHILDREN WITH THALASSEMIA AS EVALUATED BY PEDSQL AND EQ-5D-Y: A SINGLE CENTER EXPERIENCE

    Pacharapan Surapolchai, Phakatip Sinlapamongkolkul
    e2020036
    2020-06-28
    https://doi.org/10.4084/mjhid.2020.036
    1546
    PDF: 1139
    HTML: 320
  • Congenital Atypical Microcytic Anemia Accompanied by Iron Deficiency and Accumulation

    mustafa özay, zafer bıçakçı
    e2022070
    2022-08-27
    https://doi.org/10.4084/MJHID.2022.070
    866
    PDF: 589
    HTML: 312
  • INFECTIONS IN THALASSEMIA AND HEMOGLOBINOPATHIES

    Bianca Maria Ricerca, Arturo Di Girolamo, Deborah Rund
    e2009028
    2009-12-28
    1093
    PDF: 619
    HTML: 4414
  • CAN WE PREDICT INCIPIENT DIABETES MELLITUS IN PATIENTS WITH TRANSFUSION DEPENDENT β-THALASSEMIA (β-TDT) REFERRED WITH A HISTORY OF PREDIABETES? Risk factors for incipient diabetes in thalassemia

    Vincenzo De Sanctis, Ashraf Soliman, Shahina Daar, Ploutarchos Tzoulis, Christos Kattamis
    e2024005
    2024-01-01
    https://doi.org/10.4084/MJHID.2024.005
    1095
    PDF: 1354
    HTML: 112
  • VASCULAR ENDOTHELIAL GROWTH FACTOR IN CHILDREN WITH THALASSEMIA MAJOR PDF

    sameh samir fahmey, Hassan Naguib, sanna Abdelshafy, rasha Alashry
    e2013044
    2013-06-05
    https://doi.org/10.4084/mjhid.2013.044
    1332
    PDF: 877
    HTML: 1036
    Figure 1 the correlation between frequency of blood transfusion and serum vascular endothelial growth factor (VEGF).: 183
  • A MULTICENTER ICET-A STUDY ON AGE AT MENARCHE AND MENSTRUAL CYCLES IN PATIENTS WITH TRANSFUSION-DEPENDENT THALASSEMIA (TDT) WHO STARTED EARLY CHELATION THERAPY WITH DIFFERENT CHELATING AGENTS. Age at menarche and menstrual cycles in patients with transfusion-dependent thalassemia.

    SALVATORE DI MAIO, VINCENZO DE SANCTIS, PIERLUIGI MARZUILLO, CHRISTOS KATTAMIS, SHAHINA DAAR, MEHERAN KARIMI, SAKI FOROUGH, ATANAS BANKEV, VALERIA KALEVA, SOTEROULA CHRISTOU, CARMELO FORTUGNO, POLYXENI DELAPORTA, ASHRAF T SOLIMAN , PLOUTARCHOS TZOULIS
    e2023058
    2023-10-30
    https://doi.org/10.4084/MJHID.2023.058
    804
    PDF: 517
    HTML: 118
  • CONCISE REVIEW ON THE FREQUENCY, MAJOR RISK FACTORS AND SURVEILLANCE OF HEPATOCELLULAR CARCINOMA (HCC) IN ?-THALASSEMIAS: PAST, PRESENT AND FUTURE PERSPECTIVES Thalassaemia transfusion dependent, Hepatitis C, hepatocarcinoma.

    Vincenzo De Sanctis
    e2020006
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.006
    4298
    PDF: 1534
    HTML: 460
  • Concordance Rate of Fasting Plasma Glucose (PG) and 2-hour PG post Oral Glucose Tolerance Test (OGTT) in Patients with new diagnosis of Thalassemia-Related Diabetes Mellitus (Th-RDM):Implications for Clinical Practice OGTT concordance rate in thalassemia major

    Vincenzo De Sanctis, Mohammad Faranoush, Shahina Daar, Ihab Elhakim, Ashraf T Soliman, Forough Saki, Mehran Karimi, Ploutarchos Tzoulis
    e2026011
    2026-01-01
    https://doi.org/10.4084/MJHID.2026.011
    638
    PDF: 522
    Html: 110
  • A A RETROSPECTIVE LONG-TERM STUDY ON AGE AT MENARCHE AND MENSTRUAL CHARACTERISTICS IN 85 YOUNG WOMEN WITH TRANSFUSION-DEPENDENT Β-THALASSEMIA (TDT) BORN BETWEEN 1965 AND 1995 Long-Term Study on Age at Menarche and Menstrual Characteristics in patients with TDT

    Vincenzo De Sanctis, Salvatore Di Maio
    e2021040
    2021-06-28
    https://doi.org/10.4084/MJHID.2021.040
    1544
    PDF: 508
    HTML: 181
  • INSULIN-LIKE GROWTH FACTOR-1 (IGF-1): DEMOGRAPHIC, CLINICAL AND LABORATORY DATA IN 120 CONSECUTIVE ADULT PATIENTS WITH THALASSAEMIA MAJOR

    V. De Sanctis
    e2014.074
    2014-11-01
    https://doi.org/10.4084/mjhid.2014.074
    2274
    PDF: 954
    HTML: 26949
  • ACQUIRED HYPOGONADOTROPIC HYPOGONADISM (AHH) IN THALASSAEMIA MAJOR PATIENTS: AN UNDERDIAGNOSED CONDITION?

    Vincenzo De Sanctis
    e2016001
    2016-01-01
    https://doi.org/10.4084/mjhid.2016.001
    5197
    PDF: 1312
    HTML: 3589
  • INFECTIONS IN MYELODYSPLASTIC SYNDROME IN RELATION TO STAGE AND THERAPY

    Giuseppe Leone, Livio Pagano
    e2018039
    2018-07-01
    https://doi.org/10.4084/mjhid.2018.039
    4222
    PDF: 1463
    HTML: 612
  • POST-LOAD PLASMA GLUCOSE INCREASE (PG-GAP) AS A RISK FACTOR FOR DEVELOPING DYSGLYCEMIA IN PATIENTS WITH TRANSFUSION-DEPENDENT Β-THALASSEMIA (Β-TDT): RETROSPECTIVE ANALYSIS OVER 8 YEARS Post load plasma glucose increase and the risk of glucose dysregulation in thalassemia

    Vincenzo De Sanctis, Mohammad Faranoush, Efthymia Vlachaki, Theodora- Maria Venou, Ashraf T Soliman, Shahina Daar, Ploutarchos Tzoulis, Christos Kattamis
    e2025069
    2025-10-31
    https://doi.org/10.4084/MJHID.2025.069
    517
    PDF: 253
    HTML: 43
  • PATIENTS WITH HAEMOGLOBINOPATHIES AND CHRONIC HEPATITIS C: A REALLY DIFFICULT TO TREAT POPULATION IN 2016?

    Kalliopi Zachou, Pinelopi Arvaniti, Nikolaos K. Gatselis, Kalliopi Azariadis, Georgia Papadamou, Eirini Rigopoulou, George N. Dalekos
    e2017003
    2017-01-01
    https://doi.org/10.4084/mjhid.2017.003
    2958
    PDF: 988
    HTML: 2066
    Cover letter: 184
  • Does splenectomy influence the development of Hypothyroidism in Transfusion Dependent Thalassemia Patients? A retrospective study. Splenectomy in Hypothyroidism of TDT patients

    Christos KATTAMIS, Myrto Skafida, Christalena Sofocleous, Antonis Kattamis
    e2019064
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.064
    1248
    PDF: 969
    HTML: 314
  • HEMATOPOIETIC STEM CELL TRNSPLANTATION IN THALASSEMIA AND RELATED DISORDERS

    Emanuele Angelucci, Federica Pilo, Clara Targhetta, Martina Pettinau, Cristina Depau, Claudia Cogoni, Sara Usai, Mario Pani, Laura Dessì, Donatella Baronciani
    e2009015
    1422
    PDF: 492
    HTML: 3976
  • PATHOPHISIOLOGY OF SICKLE CELL DISEASE AND NEW DRUGS FOR THE TREATMENT

    Lucia De Franceschi
    e2009024
    2009-12-26
    1069
    PDF: 655
    HTML: 11083
  • Anti-mullerian hormone evaluates ovarian function in patients with non-transfusion-dependent thalassemia

    Yan Li, Kun Yang, Yali Zhou, Shiwu Cheng
    e2025007
    2024-12-31
    https://doi.org/10.4084/MJHID.2025.007
    1286
    PDF: 1218
    HTML: 181
  • The diagnostic approach to central adrenocortical insufficiency (CAI) in thalassemia

    Vincenzo De Sanctis, Heba Elsedfy, Ashraf T Soliman
    e2016026
    2016-05-01
    https://doi.org/10.4084/mjhid.2016.026
    3140
    PDF: 813
    HTML: 2775
  • THERAPEUTIC VALUE OF COMBINED THERAPY WITH DEFERASIROX AND SILYMARIN ON IRON OVERLOAD IN CHILDREN WITH BETA THALASSEMIA

    adel abd elhaleim hagag
    e2013065
    2013-11-04
    https://doi.org/10.4084/mjhid.2013.065
    2694
    PDF: 840
    HTML: 14967
    Therapeutic Value of Combined Therapy with Deferasirox and Silymarin on Iron Overload in Children with Beta Thalassemia: 321
  • Transfusion-related acute lung injury (TRALI) in two thalassaemia patients caused by the same multiparous blood donor

    George J Kontoghiorghes
    e2017060
    2017-10-18
    https://doi.org/10.4084/mjhid.2017.060
    2101
    PDF: 655
    HTML: 847
  • The IMPACT OF SUPEROXIDE DISMUTASE GENETIC POLYMORPHISM (SOD2 VAL16ALA) AND SUPEROXIDE DISMUTASE LEVEL ON DISEASE SEVERITY IN A COHORT OF EGYPTIAN SICKLE CELL DISEASE PATIENTS IN EGYPT SOD and SCD in Egypt

    Mervat Khorshied, Iman A, Shaheen, Yasmeen M.M Selim, Asmaa O. Elshahawy, Ilham Youssry
    e2022037
    2022-04-28
    https://doi.org/10.4084/MJHID.2022.037
    1139
    PDF: 591
    HTML: 432
  • Liver iron concentration and liver impairment in relation to serum IGF-1 levels in thalassaemia major patients: A retrospective study

    Vincenzo De Sanctis, Ashraf T Soliman, Giancarlo Candini, Christos Kattamis, Giuseppe Raiola, Heba Elsedfy
    e2015016
    2015-02-13
    https://doi.org/10.4084/mjhid.2015.016
    1621
    PDF: 1045
    HTML: 855
  • BONE MINERAL DENSITY AND VITAMIN D RECEPTOR GENETIC VARIANTS IN EGYPTIAN CHILDREN WITH BETA THALASSEMIA ON VITAMIN D SUPPLEMENTATION

    Hadeer A Abbassy, Reham Abdel Haleem Abo Elwafa, Omneya Magdy Omar
    e2019013
    2019-01-01
    https://doi.org/10.4084/mjhid.2019.013
    2287
    PDF: 1237
    HTML: 208
  • CLINICAL AND BIOCHEMICAL DATA OF ADULT THALASSEMIA MAJOR PATIENTS (TM) WITH MULTIPLE ENDOCRINE COMPLICATIONS (MEC) VERSUS TM PATIENTS WITH NORMAL ENDOCRINE FUNCTIONS: A RETROSPECTIVE LONG-TERM STUDY (40 YEARS) IN A TERTIARY CARE CENTER IN ITALY

    Vincenzo De Sanctis, Heba Elsedfy
    e2016022
    2016-04-12
    https://doi.org/10.4084/mjhid.2016.022
    3804
    PDF: 1036
    HTML: 3497
  • THE PERFORMANCE OF HOMA 2 COMPARED TO DYNAMIC MARKERS OF INSULIN SECRETION AND SENSITIVITY/RESISTANCE FOR PREDICTING DYSGLYCEMIA IN TRANSFUSION-DEPENDENT Β-THALASSEMIA: THE EXPERIENCE OF A SINGLE CENTRE HOMA 2 and DYNAMIC MARKERS OF INSULIN SECRETION FOR PREDICTING DYSGLYCEMIA  in TDT

    Vincenzo De Sanctis, Shahina Daar, Ploutarchos Tzoulis, Ashraf Soliman, Ihab Elhakim , Mohammad Faranoush, Christos Kattamis
    e2026055
    2026-06-30
    https://doi.org/10.4084/MJHID.2026.056
    91
    PDF: 73
    HTML: 13
  • Should every patient with MDS get iron chelation – probably yes.

    Kanjaksha Ghosh, Emanuele Angelucci, Federica Pilo, Kinjalka Ghosh
    e2017055
    2017-09-01
    https://doi.org/10.4084/mjhid.2017.055
    2344
    PDF: 954
    HTML: 379
  • LONG-TERM EFFECTIVENESS, SAFETY, AND TOLERABILITY OF TWICE-DAILY DOSING WITH DEFERASIROX IN CHILDREN WITH TRANSFUSION-DEPENDENT THALASSEMIAS UNRESPONSIVE TO STANDARD ONCE-DAILY DOSING

    Jassada Buaboonnam, Chayamon Takpradit, Vip Viprakasit, Nattee Narkbunnam, Nassawee Vathana, Kamon Phuakpet, Kleebsabai Sanpakit, Bunchoo Pongtanakul
    e2021065
    2021-10-29
    https://doi.org/10.4084/MJHID.2021.065
    1179
    PDF: 430
    HTML: 166
  • THE FREQUENCY OF ADRENAL INSUFFICIENCY IN ADOLESCENTS AND YOUNG ADULTS WITH THALASSEMIA MAJOR VERSUS THALASSEMIA INTERMEDIA IN IRAN

    Sara Matin, Masoud Ghanei Jahromi, Zohreh Karemizadeh, Sezaneh Haghpanah, Vincenzo De Sanctis, Ashraf Soliman, Mehran Karimi
    e2015005
    2014-08-28
    https://doi.org/10.4084/mjhid.2015.005
    2045
    PDF: 1083
    HTML: 9553
  • EVALUATION OF GLUTATHIONE-S-TRANSFERASE P1 POLYMORPHISM AND ITS RELATION TO BONE MINERAL DENSITY IN EGYPTIAN CHILDREN AND ADOLESCENTS WITH BETA- THALASSEMIA MAJOR

    Seham Ragab
    e2016004
    2016-01-01
    https://doi.org/10.4084/mjhid.2016.004
    3935
    PDF: 864
    HTML: 2437
    Figures: 172
  • LIVER IRON CONTENT (LIC) IN ADULTS WITH NON-TRANSFUSION DEPENDENT SICKLE CELL DISEASE (NT-SCD). CORRELATION WITH SERUM FERRITIN AND LIVER ENZYMES CONCENTRATIONS

    Vincenzo De Sanctis
    e2017037
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.037
    3935
    PDF: 988
    HTML: 1153
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