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Editor-in-Chief: Giuseppe Leone | Italy

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  • The IMPACT OF SUPEROXIDE DISMUTASE GENETIC POLYMORPHISM (SOD2 VAL16ALA) AND SUPEROXIDE DISMUTASE LEVEL ON DISEASE SEVERITY IN A COHORT OF EGYPTIAN SICKLE CELL DISEASE PATIENTS IN EGYPT SOD and SCD in Egypt

    Mervat Khorshied, Iman A, Shaheen, Yasmeen M.M Selim, Asmaa O. Elshahawy, Ilham Youssry
    e2022037
    2022-04-28
    https://doi.org/10.4084/MJHID.2022.037
    1024
    PDF: 545
    HTML: 370
  • IMPACT OF MANNOSE-BINDING PROTEIN GENE POLYMORPHISMS IN OMANI SICKLE CELL DISEASE PATIENTS

    Mathew Zachariah, Anil Pathare
    e2016013
    2016-02-11
    https://doi.org/10.4084/mjhid.2016.013
    3120
    PDF: 722
    HTML: 1562
  • THROMBOTIC MICROANGIOPATHY IN HAEMATOPOIETIC CELL TRANSPLANTATION:AN UPDATE

    Evi Stavrou, Hillard Michael Lazarus
    e2010033
    2010-10-29
    https://doi.org/10.4084/mjhid.2010.033
    1513
    PDF: 1008
    HTML: 10421
  • GENE THERAPY IN THALASSEMIA AND HEMOGLOBINOPATHIES

    Laura Breda, Roberto Gambari, Stefano Rivella
    e2009008
    2009-11-16
    1213
    PDF: 409
    HTML: 2865
  • PREVALENCE AND FACTORS ASSOCIATED WITH HUMAN PARVOVIRUS B19 INFECTION IN SICKLE CELL PATIENTS HOSPITALIZED IN TANZANIA

    Florence Urio, Humphrey George, Furahini Tluway, Thomas B Nyambo, Bruno P Mmbando, Julie Makani
    e2019054
    2019-08-29
    https://doi.org/10.4084/mjhid.2019.054
    1588
    PDF: 1173
    HTML: 197
  • THE USE OF HPLC AS A TOOL FOR NEONATAL CORD BLOOD SCREENING OF HAEMOGLOBINOPATHY - A VALIDATION STUDY

    A. Al-Madhani, Anil Pathare, Salam Alkindi
    e2019005
    2019-01-01
    https://doi.org/10.4084/mjhid.2019.005
    1882
    PDF: 1136
    HTML: 335
  • PROCALCITONIN AS A BIOMARKER OF BACTERIAL INFECTION IN SICKLE CELL VASO-OCCLUSIVE CRISIS.

    Dilip Kumar Patel, Manoj Kumar Mohapatra, Ancil George Thomas, Siris Patel, Prasanta Purohit
    e2014018
    2014-02-16
    https://doi.org/10.4084/mjhid.2014.018
    2002
    PDF: 998
    HTML: 15639
    COVER LETTER: 163
  • Association of the SOD2 polymorphism (Val6Ala) and SOD activity with vaso-occlusive crisis and acute splenic sequestration in children with sickle cell anemia

    Isabela Cristina Cordeiro Farias, Taciana Furtado Mendonça-Belmont, Andreia Soares Silva, Kleyton Palmeira do Ó, Felipe Borba Ferreira, Fernanda Silva Medeiros, Luydson Richardson Silva Vasconcelos, Moacyr Jesus Barreto de Melo Rego, Marcos Andre Cavalcanti Bezerra, Aderson Silva Araujo, Patricia Muniz Mendes Freire Moura, Ana Claudia Mendonça Anjos, Betânia Lucena Domingues Hatzlhofer, Maria do Socorro Mendonça Cavalcanti
    e2018012
    2018-02-21
    https://doi.org/10.4084/mjhid.2018.012
    2888
    PDF: 905
    HTML: 386
  • Respiratory function in pediatric African SCA patients underwent bone marrow transplantation

    Antonella Isgrò, Javid Gaziev, Marco Marziali, Katia Paciaroni, Gioia De Angelis, Cecilia Alfieri, Michela Ribersani, Festus Olusola Olowoselu, Guido Lucarelli
    e2017030
    2017-04-15
    https://doi.org/10.4084/mjhid.2017.030
    2072
    PDF: 721
    HTML: 1015
    Spirometry in SCA patients before transplant: 178
    Spirometry in SCA patients post transplant: 161
  • END-OF-LIFE CARE IN SICKLE CELL DISEASE AND TRASFUSION DEPENDEND-β-THALASSEMIA: CLINICAL, PSYCHOLOGICAL, AND ETHICAL CONSIDERATION Challenges in Supportive Care, Equity, and Compassion at End of Life

    Dr. Sophia Delicou, Dr Katerina Xydaki, Dr Maria Moraki, Dr Theodoros Aforozis
    e2026015
    2026-01-01
    https://doi.org/10.4084/MJHID.2026.015
    857
    PDF: 496
    Html: 140
  • Multiple bone and joint disease in a sickle cell anaemia patient: a case report

    John Ayodele Olaniyi, Adekunle E Alagbe, Olutoogun O Toluwalase, Olorunsogo E Busari
    e2012023
    2012-05-03
    https://doi.org/10.4084/mjhid.2012.023
    1188
    PDF: 699
    HTML: 1692
  • HOMOZYGOUS DELETION ALFA-THALASSEMIA AND HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN, TWO GENETIC FACTORS PREDICTIVE THE REDUCTION OF MORBIDITY AND MORTALITY DURING PREGNANCY IN SICKLE CELL PATIENTS . A REPORT FROM DEMOCRATIC REPUBLIC OF CONGO ALPHA THALASSEMIA AND HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN REDUCE MORBIDITY DURING PREGNANCY IN SICKLE CELL PATIENTS

    Tite Minga MIKOBI, Prosper Tshilobo LUKUSA
    e2019039
    2019-06-24
    https://doi.org/10.4084/mjhid.2019.039
    9914
    PDF: 937
    HTML: 190
  • WHAT UNRELATED HEMATOPOIETIC STEM CELL TRANSPLANTATION IN THALASSEMIA TAUGHT US ABOUT TRANSPLANT IMMUNOGENETICS.

    Giorgio La Nasa, Adriana Vacca, Roberto Littera, Eugenia Piras, Sandro Orru, Marianna Greco, Carlo Carcassi, Giovanni Caocci
    e2016048
    2016-10-20
    https://doi.org/10.4084/mjhid.2016.048
    3082
    PDF: 1096
    HTML: 1450
    Untitled: 157
    Untitled: 147
    Untitled: 147
  • RECENT INSIGHTS INTO THE POPULATION GENETICS AND DYNAMICS OF THE INHERITED DISORDERS OF HEMOGLOBIN

    David J Weatherall
    e2009022
    2009-12-20
    1011
    PDF: 438
    HTML: 516
  • Impact of hydroxyurea on clinical and biological parameters of sickle cell anemia in children in Abidjan

    MIREILLE YAYO- AYE, Adia Eusèbe Adjambri, Boidy Kouakou, Rebecca N'guessan-Blao, Louis Missa Adjé, Taïratou Kamagaté, Vincent Yapo, Duni Sawadogo
    e2024026
    2024-02-29
    https://doi.org/10.4084/MJHID.2024.026
    672
    PDF: 1047
    HTML: 60
  • SERUM TOTAL BILIRUBIN, NOT CHOLELITHIASIS, IS INFLUENCED BY UGT1A1 POLYMORPHISM, ALPHA THALASSEMIA AND ?S GENOTYPE: FIRST REPORT ON COMPARISON BETWEEN ARAB-INDIAN AND AFRICAN ?S GENES

    Said Y ALkindi, Anil Pathare, Salam Alkindi
    e2015060
    2015-10-20
    https://doi.org/10.4084/mjhid.2015.060
    1637
    PDF: 855
    HTML: 1532
  • LIVER IRON CONTENT (LIC) IN ADULTS WITH NON-TRANSFUSION DEPENDENT SICKLE CELL DISEASE (NT-SCD). CORRELATION WITH SERUM FERRITIN AND LIVER ENZYMES CONCENTRATIONS

    Vincenzo De Sanctis
    e2017037
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.037
    3694
    PDF: 923
    HTML: 1132
  • Phenotyping of Rh, Kell, Duffy and Kidd blood group antigens among non-tribal and tribal population of South Gujarat and its implication in preventing alloimmunisations in multitransfused patients.

    Avani Shah, Kanjaksha Ghosh, Preeti Sharma, Kanchan Mishra
    e2018070
    2018-10-30
    https://doi.org/10.4084/mjhid.2018.070
    1772
    PDF: 846
    HTML: 365
  • SICKLE CELL DISEASE AND PREGNANCY

    Dipty Jain, Pooja Lodha, Roshan Colah, Prachi Atmapoojya, Prachi Atmapoojya
    e2019040
    2019-06-24
    https://doi.org/10.4084/mjhid.2019.040
    5740
    PDF: 3561
    HTML: 413
  • THERAPEUTIC GENE EDITING FOR HEMOGLOBINOPATHIES Gene therapy for Hemoglobinopathies.

    Ugo Testa, Giuseppe Leone, Prof. M.D. Cappellini
    e2024068
    2024-08-31
    https://doi.org/10.4084/MJHID.2024.068
    1957
    PDF: 1153
    Html: 254
  • Genetic modulators of diversity in biological expression of sickle cell anemia in patients from democratic republic of Congo

    MAMY NGOLE, MAMY NGOLE, GLOIRE MBAYABO, PAUL LUMBALA, VALERIE RACE, NONO MVUAMA, STEPHANIE DEMAN, ERIKA SOUCHE, PROSPER TSHILOBO LUKUSA, CHRIS VAN GEET, KOENRAAD DEVRIENDT, GERT MATTHIJS, AIME LUMAKA, ISABELLE CLEYNEN
    e2025001
    2024-12-31
    https://doi.org/10.4084/MJHID.2025.001
    1590
    HTML: 213
    PDF: 1176
  • Hematological Indices of Sickle Cell Anaemia Patients with Pulmonary Tuberculosis in Northern Nigeria.

    Sagir G. Ahmed, Audu A. Bukar, Bashir Jolayemi
    e2010014
    2010-06-01
    https://doi.org/10.4084/mjhid.2010.014
    1438
    PDF: 821
    HTML: 2455
  • HEMATOPOIETIC STEM CELL TRANSPLANTATION IN EGYPT CHALLENGES AND OPPORTUNITIES

    Hossam Kamel Mahmoud, Gamaleldin Mohamed Fathy, Alaa Elhaddad, Omar Abdelrahman Fahmy, Mohamed Abdelmooti, Raafat Abdelfattah, Mahmoud Tarek Sayed Ahmed Bokhary
    e2020023
    2020-04-27
    https://doi.org/10.4084/mjhid.2020.023
    1716
    PDF: 922
    HTML: 569
  • Monocyte HLA-Dr Expression to Monitor Immune Response and Potential Infection Risks Following Vaso-Occlusive Crises in Patients with Sickle Cell Anemia Monocyte HLA-DR expression in SCA patients

    Romain Fort, Guillaume Monneret, Elie Nader, Giovanna Cannas, Philippe Connes, Fabienne Venet, Arnaud Hot
    e2022078
    2022-10-29
    https://doi.org/10.4084/MJHID.2022.078
    601
    PDF: 463
    HTML: 197
  • PARASITIC INFECTIONS IN HEMATOPOIETIC STEM CELL TRANSPLANTATION

    Isidro Jarque, Miguel Salavert, Javier Pemán
    e2016035
    2016-07-01
    https://doi.org/10.4084/mjhid.2016.035
    3611
    PDF: 1198
    HTML: 3860
    Untitled: 181
    Untitled: 240
  • CLINICAL ASPECTS OF UNCOMPLICATED AND SEVERE MALARIA

    Alessandro Bartoloni, Lorenzo Zammarchi
    e2012026
    2012-05-04
    https://doi.org/10.4084/mjhid.2012.026
    7605
    PDF: 3922
    HTML: 7276
  • Impact of Donor-Specific anti-HLA antibodies and donor KIR characteristics in haploidentical HSCT for beta-Thalassemia

    Marco Andreani, Manuela Testi, Pietro Sodani, Maria Troiano, Andrea Di Luzio, Giuseppe Testa, Michela Falco, Elvira Poggi, Javid Gaziev, Antonina Piazza
    e2017020
    2017-03-01
    https://doi.org/10.4084/mjhid.2017.020
    2840
    PDF: 920
    HTML: 518
  • RELIABILITY OF DIFFERENT RBC INDICES AND FORMULAS IN DISCRIMINATING BETWEEN ?-THALASSEMIA MINOR AND OTHER CAUSES OF MICROCYTIC HYPOCHROMIC ANEMIA

    Elahe Bordbar, Mehdi Taghipour, Beth E Zucconi
    e2015022
    2015-02-13
    https://doi.org/10.4084/mjhid.2015.022
    1885
    PDF: 1584
    HTML: 14601
    Untitled: 183
    Untitled: 153
  • CLINICAL AND LABORATORY FEATURES OF SICKLE CELL DISEASE S/D PUNJAB: IMPACT OF HBF AND HYDROXYUREA SCD S/D Punjab

    r. Salam Al-Kindi, Isra Al-Busaidi, Anil Pathare
    e2024046
    2024-04-30
    https://doi.org/10.4084/MJHID.2024.046
    1251
    PDF: 1076
    HTML: 88
  • NURSING MANAGEMENT OF HAEMORRHAGIC CYSTITIS IN PATIENTS UNDERGOING HAEMATOPOIETIC STEM CELL TRANSPLANTATION: A MULTICENTRE ITALIAN SURVEY Nursing management of haemorrhagic cystitis

    alvisa palese, chiara visintini, margherita venturini, gianpaolo gargiulo, stefano botti
    e2019051
    2019-08-29
    https://doi.org/10.4084/mjhid.2019.051
    1699
    PDF: 1005
    HTML: 213
  • HEMATOPOIETIC CELL TRANSPLANTATION FOR OLDER PATIENTS WITH MDS

    Mazyar Shadman, Joachim Deeg
    e2014056
    2014-09-01
    https://doi.org/10.4084/mjhid.2014.056
    1914
    PDF: 729
    HTML: 3098
  • GROUP-BASED TRAJECTORY MODELING OF PLATELET IN PATIENTS WITH APLASTIC ANEMIA: A STUDY BASED ON THE MIMIC DATABASE

    Lang Peng, Lixin Zou, Xiaoliu Liu
    e2025012
    2025-02-27
    https://doi.org/10.4084/MJHID.2025.012
    918
    PDF: 929
    Suppl. Files: 612
    HTML: 87
  • Clinical and laboratory features of Hemoglobin La Desirade variant in association with sickle cell and alpha thalassemia genes Clinical & laboratory features of Hb La Desirade trait and compound heterozygous for Hb La Desirade and HbS Hemoglobin.

    Salam Alkindi, Shoaib Al Zadjali, Mohamed Al Rawahi , Hamoud Al Haddabi, Shahina Daar, Refaat Abdullah Elsadek, Bahaa Eldeen Diab Sherkawy, Anil Pathare
    e2021010
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.010
    1478
    PDF: 417
    HTML: 201
  • BACK TO THE “GOLD STANDARD”: HOW PRECISE IS HEMATOCRIT DETECTION TODAY? Novel ImageJ-based approach for the precise hematocrit measurement

    Dr. Leonid Livshits, Ms. Tal Bilu, Ms. Sari Peretz, Prof. Anna Bogdanova, Prof. Max Gassmann, Dr. Harel Eitam, Prof. Ariel Koren, Prof. Carina Levin
    e2022049
    2022-06-29
    https://doi.org/10.4084/MJHID.2022.049
    1648
    PDF: 754
    HTML: 424
  • PREVALENCE OF HEPATITIS B, HEPATITIS C AND HIV IN MULTIPLY TRANSFUSED SICKLE CELL DISEASE PATIENTS FROM OMAN HBV,HCV and HIV and Sickle Cell Disease.

    Anil Pathare, Salam Alkindi, prof.
    e2019058
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.058
    1513
    PDF: 951
    HTML: 337
  • A MULTICENTRE ICET-A STUDY OF CONFIRMED SARS-COV-2 INFECTION IN PATIENTS WITH HEMOGLOBINOPATHIES: PRELIMINARY DATA FROM 10 COUNTRIES

    Vincenzo De Sanctis
    e2020046
    2020-06-28
    https://doi.org/10.4084/mjhid.2020.046
    2653
    PDF: 1531
    HTML: 286
  • FINE MAPPING OF GLUCOSE 6 PHOSPHATE DEHYDROGENASE (G6PD) DEFICIENCY IN RURAL AREA OF SOUTH WEST ODISHA USING THE CLINICAL, HEMATOLOGICAL AND MOLECULAR APPROACH

    Ravindra Kumar, MPSS Singh, Soumendu Mahapatra, Sonam Chourasia, Malay Kumar Tripathi, John Oommen, Praveen Kumar Bharti, Rajasubramaniam Shanmugam
    e2020015
    2020-02-26
    https://doi.org/10.4084/mjhid.2020.015
    1651
    PDF: 975
    HTML: 508
  • ACUTE LUNG INJURY COMPLICATING BLOOD TRANSFUSION IN POST-PARTUM HEMORRHAGE: INCIDENCE AND RISK FACTORS.

    Luciana Teofili, Maria Bianchi, Bruno A Zanfini, Stefano Catarci, Rossella Sicuranza, Serena Spartano, Gina Zini, Gaetano Draisci
    e2014069
    2014-10-22
    https://doi.org/10.4084/mjhid.2014.069
    2318
    PDF: 1166
    HTML: 3583
    Acute lung injury complicating blood transfusion in post-partum hemorrhage: incidence and risk factors.: 393
  • PREVALENCE OF HEPATITIS C AMONG EGYPTIAN CHILDREN WITH SICKLE CELL DISEASE AND THE ROLE OF IL28B GENE POLYMORPHISMS IN SPONTANEOUS VIRAL CLEARANCE

    Somaia Mohammed Mousa, Mona Kamal El-Ghamrawy, Heba Gouda, Mervat Khorshied, Dina Ahmed, Hala Shiba
    e2016007
    2016-01-01
    https://doi.org/10.4084/mjhid.2016.007
    3766
    PDF: 764
    HTML: 2443
  • MYELODYSPLASTIC SYNDROMES AND IRON CHELATION THERAPY

    Emanuele Angelucci, Silvana Anna Maria Urru, Federica Pilo, Alberto Piperno
    e2017021
    2017-03-01
    https://doi.org/10.4084/mjhid.2017.021
    3292
    PDF: 1245
    HTML: 1843
    Fig.1: 177
    Fig. 2: 184
  • CARDIAC FUNCTION AND IRON CHELATION IN THALASSEMIA MAJOR AND INTERMEDIA: A REVIEW OF THE UNDERLYING PATHOPHYSIOLOGY AND APPROACH TO CHELATION MANAGEMENT

    Athanasios Aessopos, Vasilios Berdoukas
    e2009002
    2009-07-18
    1507
    PDF: 461
    HTML: 1423
  • ?-THALASSEMIA DISTRIBUTION IN THE OLD WORLD: A HISTORICAL STANDPOINT OF AN ANCIENT DISEASE

    Vincenzo De Sanctis
    e2017018
    2017-02-20
    https://doi.org/10.4084/mjhid.2017.018
    10771
    PDF: 4190
    HTML: 4307
  • DEFERASIROX: OVER A DECADE OF EXPERIENCE IN THALASSEMIA

    Ali Taher
    e2018066
    2018-11-01
    https://doi.org/10.4084/mjhid.2018.066
    2734
    PDF: 1530
    HTML: 215
  • SURVIVAL PROBABILITY IN PATIENTS WITH SICKLE CELL ANEMIA USING THE COMPETITIVE RISK STATISTICAL MODEL

    Samir Ballas, Emilia Matos do Nascimento, PhD, Clarisse Lopes de Castro Lobo, MD, Basilio de Bragança Pereira, PhD
    e2019022
    2019-02-26
    https://doi.org/10.4084/mjhid.2019.022
    1443
    PDF: 891
    HTML: 179
  • Hyperhemolytic Syndrome complicating a Delayed Hemolytic Transfusion Reaction due to anti-P1 alloimmunization, in a pregnant woman with HbO-Arab?-thalassemia

    Zoe Bezirgiannidou, Anna Christoforidou, Eftychia Kontekaki, Athanasios Anastasiadis, Spyros Papamichos, Helen Menexidou, Dimitrios Margaritis, George Martinis, Elpidoforos Mandadakis
    e2016053
    2016-10-18
    https://doi.org/10.4084/mjhid.2016.053
    3050
    PDF: 842
    HTML: 1235
    Figure 1: 132
  • EVOLUTION OF HEMOGLOBINOPATHY PREVENTION IN AFRICA

    Slaheddine Fattoum
    e2009005
    2009-10-27
    991
    PDF: 406
    HTML: 14963
  • Safety warning for ChAdOx1 nCov-19 vaccine in patients with sickle cell disease Astra Zeneca vaccine in Sickle cell disease (SCD)

    Salam Alkindi, Dr. , Dr.
    e2021059
    2021-09-01
    https://doi.org/10.4084/MJHID.2021.059
    1981
    PDF: 450
    HTML: 115
  • STUDY OF SERUM HAPTOGLOBIN LEVEL AND ITS RELATION TO ERYTHROPOIETIC ACTIVITY IN BETA THALASSEMIA CHILDREN .

    Seham Ragab, Manal A. Safan, Eman A. Badr
    e2015019
    2015-02-12
    https://doi.org/10.4084/mjhid.2015.019
    2074
    PDF: 1127
    HTML: 2567
    Study of serum haptoglobin level in thalassemia: 311
    Figures: 155
  • THE HISTORY OF DEFERIPRONE (L1) AND THE COMPLETE TREATMENT OF IRON OVERLOAD IN THALASSAEMIA The history and roles of deferiprone

    George J Kontoghiorghes, Marios Kleanthous, Christina N. Kontoghiorghe
    e2020011
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.011
    2216
    PDF: 1534
    HTML: 570
  • VASCULAR ENDOTHELIAL GROWTH FACTOR IN CHILDREN WITH THALASSEMIA MAJOR PDF

    sameh samir fahmey, Hassan Naguib, sanna Abdelshafy, rasha Alashry
    e2013044
    2013-06-05
    https://doi.org/10.4084/mjhid.2013.044
    1227
    PDF: 807
    HTML: 1022
    Figure 1 the correlation between frequency of blood transfusion and serum vascular endothelial growth factor (VEGF).: 150
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