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Editor-in-Chief: Giuseppe Leone | Italy

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  • The INFLUENCE OF NUTRITION ON DISEASE SEVERITY AND HEALTH-RELATED QUALITY OF LIFE IN ADULTS WITH SICKLE CELL DISEASE A Prospective Longitudinal Study

    Sanaa Kamal, Moheyeldeen Mohamed Naghib, Jamaan Al Zahrani, Huda Hassan, Karim Abdel Aziz Moawado, Omar Arrahman
    e2021007
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.007
    2175
    PDF: 877
    HTML: 283
  • THE EFFECT OF ALPHA THALASSEMIA, HBF and HBC ON HAEMATOLOGICAL PARAMETERS OF SICKLE CELL DISEASE PATIENTS IN IBADAN, NIGERIA. ALPHA THALASSEMIA, HBF and HBC ON HAEMATOLOGICAL PARAMETERS OF SICKLE CELL DISEASE PATIENTS

    FASOLA ATINUKE
    e2022001
    2022-01-01
    https://doi.org/10.4084/MJHID.2022.001
    2143
    PDF: 916
    HTML: 55
  • NEW THERAPEUTIC OPTIONS FOR THE TREATMENT OF SICKLE CELL DISEASE Guest Editor: Raffaella Origa

    Alessandro Matte, Filippo Mazzi, Enrica Federti, Oliviero Olivieri, Lucia De Franceschi
    e2019002
    2019-01-01
    https://doi.org/10.4084/mjhid.2019.002
    6649
    PDF: 3539
    HTML: 718
  • RENAL ABNORMALITIES AMONG SICKLE CELL DISEASE PATIENTS IN A POOR MANAGEMENT SETTING: A SURVEY IN THE DEMOCRATIC REPUBLIC OF THE CONGO

    Paul Kambale-Kombi, Roland Marini Djang’eing’a, Jean-Pierre Alworong’a Opara, Jean-Paulin Mbo Mukonkole, Vincent Bours, Dieu-Merci Mbumba Lupaka, Serge Tonen-Wolyec, Lucien Bolukaoto Bome, Charles Kayembe Tshilumba, Salomon Batina-Agasa
    e2022046
    2022-06-29
    https://doi.org/10.4084/MJHID.2022.046
    789
    PDF: 611
    HTML: 327
  • ENDOTHELIAL NITRIC OXIDE SYNTHASE (ENOS) GENE POLYMORPHISM IS ASSOCIATED WITH AGE ONSET OF MENARCHE IN SICKLE CELL DISEASE FEMALES OF INDIA

    Sudhansu Sekhar Nishank
    e2013036
    2013-06-04
    https://doi.org/10.4084/mjhid.2013.036
    1431
    PDF: 897
    HTML: 2346
    Table: 174
  • THE ROLE OF INFECTION IN THE PATHOGENESIS OF VASO-OCCLUSIVE CRISIS IN PATIENTS WITH SICKLE CELL DISEASE.

    Sagir Gumel Ahmed
    e2011028
    2011-07-08
    https://doi.org/10.4084/mjhid.2011.028
    5039
    PDF: 1286
    HTML: 2721
    Cover letter: 173
  • LIVER DISEASE & SICKLE CELL DISEASE: AUTOIMMUNE HEPATITIS MORE THAN A COINCIDENCE; A SYSTEMATIC LITERATURE REVIEW.

    Kelvin Lynch, Andrea Mega, Andrea Piccin, Massimo Daves, Helen Fogarty
    e2023060
    2023-10-30
    https://doi.org/10.4084/MJHID.2023.060
    2008
    PDF: 925
    HTML: 210
  • CHARACTERIZATION AND ANTIMICROBIAL SUSCEPTIBILITY PROFILE OF SEPTICAEMIA-CAUSING PATHOGENS ISOLATED FROM FEBRILE CHILDREN WITH SICKLE CELL DISEASE IN KANO, NIGERIA.

    Ibrahim Yusuf
    e2018016
    2018-02-15
    https://doi.org/10.4084/mjhid.2018.016
    2765
    PDF: 942
    HTML: 503
  • INCREASED VASOOCCLUSIVE CRISIS IN “O” BLOOD GROUP SICKLE CELL DISEASE PATIENTS: ASSOCIATION WITH UNDERLYING THROMBOSPONDIN LEVELS.

    M. Al Huneini, Anil Pathare
    e2017028
    2017-04-20
    https://doi.org/10.4084/mjhid.2017.028
    1895
    PDF: 880
    HTML: 1346
  • IMPACT OF MANNOSE-BINDING PROTEIN GENE POLYMORPHISMS IN OMANI SICKLE CELL DISEASE PATIENTS

    Mathew Zachariah, Anil Pathare
    e2016013
    2016-02-11
    https://doi.org/10.4084/mjhid.2016.013
    3123
    PDF: 723
    HTML: 1564
  • SICKLE CELL DISEASE AND VENOUS THROMBOEMBOLISM

    Zohreh Rahimi, Abbas Parsian
    e2011024
    2011-05-23
    https://doi.org/10.4084/mjhid.2011.024
    2152
    PDF: 825
    HTML: 2057
  • Sickle Cell Disease: Management options and challenges in developing countries

    Daniel Ansong, Alex Osei-Akoto, Delaena Ocloo, Kwaku Ohene-Frempong Ohene-Frempong
    e2013062
    2013-11-04
    https://doi.org/10.4084/mjhid.2013.062
    2342
    PDF: 1213
    HTML: 983
  • DISTRIBUTION OF DNA DAMAGE REPAIR GENE POLYMORPHISM hOGG1, XRCC1 and p53 AMONG SICKLE CELL DISEASE PATIENTS IN INDIA

    Sudhansu Sekhar Nishank
    e2015046
    2015-07-02
    https://doi.org/10.4084/mjhid.2015.046
    1454
    PDF: 756
    HTML: 1458
    Table Genotype and allele frequencies of hOGG1 codon 326 Ser>Cys and p53 72Arg>Pro polymorphisms among SCD patients and control group: 160
  • CURRENT ISSUES AND OPTIONS FOR HORMONAL CONTRACEPTION IN ADOLESCENTS AND YOUNG ADULT WOMEN WITH SICKLE CELL DISEASE: AN UPDATE FOR HEALTH CARE PROFESSIONALS Hormonal Contraception in Adolescents and Young Adult Women With Sickle Cell Disease

    Vincenzo De Sanctis
    e2020032
    2020-04-27
    https://doi.org/10.4084/mjhid.2020.032
    2055
    PDF: 1365
    HTML: 671
  • HEALTH-RELATED QUALITY OF LIFE MEASUREMENT IN ADULTS WITH SICKLE CELL DISEASE IN STEADY STATE: EXPERIENCE OF ONE FRENCH REFERENCE CENTER

    Giovanna Cannas, Solene Poutrel, Emilie Virot, Manon Marie, Alexandre Guilhem, Amal El-Kanouni, Richard Bourgeay, Marie-Grace Mutumwa, Mohamed Elhamri, Arnaud Hot
    e2025065
    2025-08-31
    https://doi.org/10.4084/MJHID.2025.065
    873
    PDF: 460
    Html: 128
  • INFECTIONS IN THALASSEMIA AND HEMOGLOBINOPATHIES

    Bianca Maria Ricerca, Arturo Di Girolamo, Deborah Rund
    e2009028
    2009-12-28
    1034
    PDF: 590
    HTML: 4261
  • PERIOPERATIVE MANAGEMENT OF SICKLE CELL DISEASE: A NARRATIVE REVIEW

    Kwame Ofori Adjepong, Folashade Otegbeye, Yaw Amoateng ADJEPONG
    e2018032
    2018-05-01
    https://doi.org/10.4084/mjhid.2018.032
    7794
    PDF: 3163
    HTML: 1166
  • CLINICAL AND LABORATORY FEATURES OF SICKLE CELL DISEASE S/D PUNJAB: IMPACT OF HBF AND HYDROXYUREA SCD S/D Punjab

    r. Salam Al-Kindi, Isra Al-Busaidi, Anil Pathare
    e2024046
    2024-04-30
    https://doi.org/10.4084/MJHID.2024.046
    1254
    PDF: 1078
    HTML: 89
  • PREVALENCE AND FACTORS ASSOCIATED WITH HUMAN PARVOVIRUS B19 INFECTION IN SICKLE CELL PATIENTS HOSPITALIZED IN TANZANIA

    Florence Urio, Humphrey George, Furahini Tluway, Thomas B Nyambo, Bruno P Mmbando, Julie Makani
    e2019054
    2019-08-29
    https://doi.org/10.4084/mjhid.2019.054
    1591
    PDF: 1177
    HTML: 199
  • The IMPACT OF SUPEROXIDE DISMUTASE GENETIC POLYMORPHISM (SOD2 VAL16ALA) AND SUPEROXIDE DISMUTASE LEVEL ON DISEASE SEVERITY IN A COHORT OF EGYPTIAN SICKLE CELL DISEASE PATIENTS IN EGYPT SOD and SCD in Egypt

    Mervat Khorshied, Iman A, Shaheen, Yasmeen M.M Selim, Asmaa O. Elshahawy, Ilham Youssry
    e2022037
    2022-04-28
    https://doi.org/10.4084/MJHID.2022.037
    1028
    PDF: 546
    HTML: 372
  • PERCEPTION OF COMMUNITY HEALTH CARE WORKERS ABOUT PATIENTS WITH SICKLE CELL DISEASE IN PRIMARY HEALTH CARE AFTER AN EDUCATIONAL INTERVENTION

    Ludmila Mourão Xavier Gomes, Marcos Borato Viana, Igor Alcântara Pereira
    22015031
    2015-04-19
    https://doi.org/10.4084/mjhid.2015.031
    1997
    PDF: 931
    HTML: 1646
  • PREVALENCE AND AETIOLOGY OF BACTEREMIA IN FEBRILE CHILDREN WITH SICKLE CELL DISEASE AT A NIGERIA TERTIARY HOSPITAL

    Biobele Jotham Brown, Hannah O Dada-Adegbola, Catherine Trippe, Olufunmilayo Olopade
    e2017039
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.039
    2846
    PDF: 1162
    HTML: 989
  • PREVALENCE OF HEPATITIS B, HEPATITIS C AND HIV IN MULTIPLY TRANSFUSED SICKLE CELL DISEASE PATIENTS FROM OMAN HBV,HCV and HIV and Sickle Cell Disease.

    Anil Pathare, Salam Alkindi, prof.
    e2019058
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.058
    1517
    PDF: 954
    HTML: 337
  • A MULTICENTRE ICET-A STUDY OF CONFIRMED SARS-COV-2 INFECTION IN PATIENTS WITH HEMOGLOBINOPATHIES: PRELIMINARY DATA FROM 10 COUNTRIES

    Vincenzo De Sanctis
    e2020046
    2020-06-28
    https://doi.org/10.4084/mjhid.2020.046
    2661
    PDF: 1532
    HTML: 286
  • SICKLE CELL DISEASE AND PREGNANCY

    Dipty Jain, Pooja Lodha, Roshan Colah, Prachi Atmapoojya, Prachi Atmapoojya
    e2019040
    2019-06-24
    https://doi.org/10.4084/mjhid.2019.040
    5770
    PDF: 3565
    HTML: 414
  • TRANSFUSION PRACTICE, POST-TRANSFUSION COMPLICATIONS AND RISK FACTORS IN SICKLE CELL DISEASE IN SENEGAL, WEST AFRICA.

    Moussa Seck, Alioune Badara Senghor, Mossane Loum, Sokhna Aissatou Touré, Blaise Félix Faye, Alioune Badara Diallo, Mohamed Keita, Elimane Seydi Bousso, Sérigne Mourtalla Guèye, Macoura Gadji, Abibatou Sall, Awa Oumar Touré, Saliou Diop
    e2022004
    2022-01-01
    https://doi.org/10.4084/MJHID.2022.004
    1699
    PDF: 929
    HTML: 359
  • PREVALENCE OF HEPATITIS C AMONG EGYPTIAN CHILDREN WITH SICKLE CELL DISEASE AND THE ROLE OF IL28B GENE POLYMORPHISMS IN SPONTANEOUS VIRAL CLEARANCE

    Somaia Mohammed Mousa, Mona Kamal El-Ghamrawy, Heba Gouda, Mervat Khorshied, Dina Ahmed, Hala Shiba
    e2016007
    2016-01-01
    https://doi.org/10.4084/mjhid.2016.007
    3771
    PDF: 771
    HTML: 2444
  • IMPACT OF RED CELL EXCHANGE TRANSFUSION ON INFLAMMATORY MARKERS IN SICKLE CELL DISEASE

    Adriana Costa, Inês Mendes, Joana Lage, Marta Moniz, Catarina Amorim, Pedro Nunes, Helena Almeida, Carlos Escobar, Ana Ventura, Teresa Ferreira
    e2025011
    2024-12-31
    https://doi.org/10.4084/MJHID.2025.011
    1735
    PDF: 1282
    HTML: 205
  • IRON METABOLISM IN THALASSEMIA AND SICKLE CELL DISEASE

    Raffaella Mariani, Paola Trombini, Matteo Pozzi, Alberto Piperno
    e2009006
    2009-10-27
    1557
    PDF: 625
    HTML: 43872
  • TREOSULFAN-BASED CONDITIONING REGIMEN IN SIBLING AND ALTERNATIVE DONOR HEMATOPOIETIC STEM CELL TRANSPLANTATION FOR CHILDREN WITH SICKLE CELL DISEASE

    Antonio Marzollo, Elisabetta Calore, Manuela Tumino, Marta Pillon, Maria Vittoria Gazzola, Roberta Destro, Raffaella Colombatti, Piero Marson, Tiziana Tison, Anna Colpo, Chiara Mainardi, Maria Gabelli, Maria Paola Boaro, Sara Rossin, Aurora Strano, Nadia Quaglia, Federica Menzato, Giuseppe Basso, Laura Sainati, Chiara Messina
    e2017014
    2017-02-15
    https://doi.org/10.4084/mjhid.2017.014
    4109
    PDF: 1342
    HTML: 1148
  • THERAPEUTIC GENE EDITING FOR HEMOGLOBINOPATHIES Gene therapy for Hemoglobinopathies.

    Ugo Testa, Giuseppe Leone, Prof. M.D. Cappellini
    e2024068
    2024-08-31
    https://doi.org/10.4084/MJHID.2024.068
    1968
    PDF: 1157
    Html: 255
  • LIVER IRON CONTENT (LIC) IN ADULTS WITH NON-TRANSFUSION DEPENDENT SICKLE CELL DISEASE (NT-SCD). CORRELATION WITH SERUM FERRITIN AND LIVER ENZYMES CONCENTRATIONS

    Vincenzo De Sanctis
    e2017037
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.037
    3706
    PDF: 924
    HTML: 1132
  • CURING HEMOGLOBINOPATHIES: CHALLENGES AND ADVANCES OF CONVENTIONAL AND NEW GENE THERAPY APPROACHES.

    Irene Motta, Valentina Ghiaccio, Andrea Cosentino, Laura Breda
    e2019067
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.067
    2766
    PDF: 1777
    HTML: 725
  • PATHOPHISIOLOGY OF SICKLE CELL DISEASE AND NEW DRUGS FOR THE TREATMENT

    Lucia De Franceschi
    e2009024
    2009-12-26
    1022
    PDF: 636
    HTML: 11053
  • How I treat acute and persistent sickle cell pain

    Samir Ballas
    e2020064
    2020-09-08
    https://doi.org/10.4084/mjhid.2020.064
    1818
    PDF: 1077
    HTML: 456
  • PATTERN OF CEREBRAL BLOOD FLOW VELOCITY USING TRANSCRANIAL DOPPLER ULTRASONOGRAPHY IN CHILDREN WITH SICKLE CELL DISORDER IN LAGOS STATE, NIGERIA

    Motunrayo Oluwabukola Adekunle
    e2017050
    2017-08-14
    https://doi.org/10.4084/mjhid.2017.050
    1921
    PDF: 787
    HTML: 803
  • Multiple bone and joint disease in a sickle cell anaemia patient: a case report

    John Ayodele Olaniyi, Adekunle E Alagbe, Olutoogun O Toluwalase, Olorunsogo E Busari
    e2012023
    2012-05-03
    https://doi.org/10.4084/mjhid.2012.023
    1196
    PDF: 699
    HTML: 1694
  • FOETAL HAEMOGLOBIN AND DISEASE SEVERITY IN NIGERIAN CHILDREN WITH SICKLE CELL ANAEMIA.

    Oluwagbemiga Adeodu, Morenike Akinlosotu, Samuel Adegoke, Saheed Oseni
    e2017063
    2017-11-01
    https://doi.org/10.4084/mjhid.2017.063
    5475
    PDF: 998
    HTML: 936
  • PREVALENCE OF SERIOUS BACTERIAL INFECTIONS IN CHILDREN WITH SICKLE CELL DISEASE AT KING ABDULAZIZ HOSPITAL, AL AHSA Bacterial infections in children with sickle cell diseas

    Manal Alsaif, Joan Robinson, Moshtag Abdulbaqi, Mustafa Aghbari, Khalid Al Noaim, Muneera Alabdulqader
    e2021002
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.002
    1399
    PDF: 530
    HTML: 195
  • CLINICAL SIGNIFICANCE OF ASSESSMENT OF THROMBOSPONDIN AND PLACENTA GROWTH FACTOR LEVELS IN PATIENTS WITH SICKLE CELL ANEMIA: TWO CENTERS EGYPTIAN STUDIES

    adel abd elhaleim hagag, Ghada Elmashad, Aml Ezzat Abd El-Lateef
    e2014044
    2014-06-29
    https://doi.org/10.4084/mjhid.2014.044
    1715
    PDF: 883
    HTML: 2219
  • HEMATOPOIETIC STEM CELL TRANSPLANTATION IN SEVERE PEDIATRIC SICKLE CELL DISEASE: OUTCOME AND LONG-TERM COMPLICATIONS, SAUDI EXPERIENCE AT KING FAISAL SPECIALIST HOSPITAL, RIYADH, SAUDI ARABIA HCT in in Severe Pediatric Sickle Cell Disease

    Abdullah Al-Jefri, Fatema Al-Hashem, Khawar, Amal Al-Seraihy, Ali Al-Ahmari, Ibrahim Ghemlas, Awatif AlAnazi, Hawazen Al-Saedi, Saadiya Khan, Abdulrahman Al-Musa, Mahasen Saleh, Mouhab Ayas
    e2025030
    2025-04-30
    https://doi.org/10.4084/MJHID.2025.030
    1054
    PDF: 851
    HTML: 320
  • END-OF-LIFE CARE IN SICKLE CELL DISEASE AND TRASFUSION DEPENDEND-β-THALASSEMIA: CLINICAL, PSYCHOLOGICAL, AND ETHICAL CONSIDERATION Challenges in Supportive Care, Equity, and Compassion at End of Life

    Dr. Sophia Delicou, Dr Katerina Xydaki, Dr Maria Moraki, Dr Theodoros Aforozis
    e2026015
    2026-01-01
    https://doi.org/10.4084/MJHID.2026.015
    873
    PDF: 510
    Html: 141
  • HOMOZYGOUS DELETION ALFA-THALASSEMIA AND HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN, TWO GENETIC FACTORS PREDICTIVE THE REDUCTION OF MORBIDITY AND MORTALITY DURING PREGNANCY IN SICKLE CELL PATIENTS . A REPORT FROM DEMOCRATIC REPUBLIC OF CONGO ALPHA THALASSEMIA AND HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN REDUCE MORBIDITY DURING PREGNANCY IN SICKLE CELL PATIENTS

    Tite Minga MIKOBI, Prosper Tshilobo LUKUSA
    e2019039
    2019-06-24
    https://doi.org/10.4084/mjhid.2019.039
    9924
    PDF: 938
    HTML: 191
  • ALLOIMMUNIZATION IN PATIENTS WITH SICKLE CELL DISEASE AND THALASSAEMIA: EXPERIENCE OF SINGLE CENTRE FROM OMAN

    Anil Pathare, Salam Alkindi
    e2017013
    2017-02-15
    https://doi.org/10.4084/mjhid.2017.013
    2596
    PDF: 1210
    HTML: 1738
  • GENE THERAPY IN THALASSEMIA AND HEMOGLOBINOPATHIES

    Laura Breda, Roberto Gambari, Stefano Rivella
    e2009008
    2009-11-16
    1220
    PDF: 409
    HTML: 2866
  • A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β⁺-Thalassaemia Patient

    Marta Bortolotti, Gianluca Costamagna, Marta Mancarella, Delia Gagliardi, Silvia Lanfranconi, Alessia Marcon, Margherita Migone De Amicis, Nereo Bresolin, Stefania Corti, Giovanna Graziadei
    e2022019
    2022-02-27
    https://doi.org/10.4084/MJHID.2022.019
    918
    PDF: 499
    HTML: 224
  • SICKLE CELL TRAIT, CLINICAL MANIFESTATIONS AND OUTCOMES: A CROSS-SECTIONAL STUDY

    Diego A Vargas-Hernández, Adriana Catalina Uscategui-Ruiz, Andrés Jesus Prada-Rueda , Consuelo Romero-Sánchez
    e2023015
    2023-02-28
    https://doi.org/10.4084/MJHID.2023.015
    1541
    PDF: 1054
    HTML: 451
  • The COVID-19 in Omani children with chronic Hemato-oncology diseases COVID-19 in Omani children with chronic Hemato-oncology diseases

    Laila Al Yazidi
    e2020074
    2020-10-27
    https://doi.org/10.4084/mjhid.2020.074
    759
    PDF: 658
    HTML: 290
  • Safety warning for ChAdOx1 nCov-19 vaccine in patients with sickle cell disease Astra Zeneca vaccine in Sickle cell disease (SCD)

    Salam Alkindi, Dr. , Dr.
    e2021059
    2021-09-01
    https://doi.org/10.4084/MJHID.2021.059
    1992
    PDF: 450
    HTML: 115
  • TRANSIENT ELASTOGRAPHY (TE) IS A USEFUL TOOL FOR ASSESSING THE RESPONSE OF LIVER IRON CHELATION IN SICKLE CELL DISEASE PATIENTS

    SOPHIA DELICOU
    e2018049
    2018-09-01
    https://doi.org/10.4084/mjhid.2018.049
    1465
    PDF: 770
    HTML: 172
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