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Peripheral Red Blood Cell Split Chimerism as a Consequence of Intramedullary Selective Apoptosis of Recipient Red Blood Cells in a Case of Sickle Cell Disease

Marco Marziali, Antonella Isgrò, Pietro Sodani, Javid Gaziev, Daniela Fraboni, Katia Paciaroni, Cristiano Gallucci, Cecilia Alfieri, Andrea Roveda, Gioia De Angelis, Luisa Cardarelli, Michela Ribersani, Marco Andreani, Guido Lucarelli
Abstract 1367 | PDF Downloads 745 HTML Downloads 1809 Untitled Downloads 0 Untitled Downloads 0

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DOI: https://doi.org/10.4084/mjhid.2014.066

JUSTIFICATION OF UNIVERSAL IRON SUPPLEMENTATION FOR INFANTS 6-12 MONTHS IN REGIONS WITH A HIGH PREVALENCE OF THALASSEMIA

Phakatip Sinlapamongkolkul, Pacharapan Surapolchai, Vip Viprakasit
Abstract 671 | PDF Downloads 433 Suppl. Files Downloads 214 HTML Downloads 129

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DOI: https://doi.org/10.4084/MJHID.2023.056

THE COURSE OF HEPATITIS C INFECTION AND RESPONSE TO ANTI-VIRAL THERAPY IN PATIENTS WITH THALASSEMIA MAJOR AND HEPATITIS C INFECTION: A LONGITUDINAL, PROSPECTIVE STUDY.

Sanaa Kamal, Sara Abdelhakam, Dr., Dahlia Ghoraba, Mohamad Amer Mohsen, Ahmed Abdelsalam, Huda Hassan, Leila Nabeigh
Abstract 1073 | PDF Downloads 843 HTML Downloads 135

Page e2019060

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DOI: https://doi.org/10.4084/mjhid.2019.060

PREVALENCE OF THALASSEMIA IN THE VIETNAMESE POPULATION AND BUILDING A CLINICAL DECISION SUPPORT SYSTEM FOR PRENATAL SCREENING FOR THALASSEMIA

Danh Cuong Tran, Anh Linh Dang, Thi Ngoc Lan Hoang, Chi Thanh Nguyen, Thi Ngoc Mai Dinh, Van Anh Tran, Thi Kim Phuong Doan, Thi Trang Nguyen
Abstract 1002 | HTML Downloads 195 PDF Downloads 812

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DOI: https://doi.org/10.4084/MJHID.2023.026

QUALITY OF LIFE IN PATIENTS WITH THALASSEMIA MAJOR AND INTERMEDIA IN KERMAN-IRAN (I.R.)

Hossein Safizadeh, Zahra Farahmandinia, Simin Soltani nejad, Nasim Pourdamghan, Majid Araste
Abstract 1326 | PDF Downloads 603 HTML Downloads 2282 Cover Letter Downloads 0

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DOI: https://doi.org/10.4084/mjhid.2012.058

SPECTRUM OF BETA GLOBIN GENE MUTATIONS IN EGYPTIAN CHILDREN WITH ?- THALASSEMIA

MR El-Shanshory, Adel Abd Elhaleim Hagag
Abstract 1607 | PDF Downloads 828 HTML Downloads 4137

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DOI: https://doi.org/10.4084/mjhid.2014.071

STUDY OF SERUM HAPTOGLOBIN LEVEL AND ITS RELATION TO ERYTHROPOIETIC ACTIVITY IN BETA THALASSEMIA CHILDREN .

Seham Ragab, Manal A. Safan, Eman A. Badr
Abstract 1823 | PDF Downloads 976 HTML Downloads 2542 Study of serum haptoglobin level in thalassemia Downloads 0 Figures Downloads 0

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DOI: https://doi.org/10.4084/mjhid.2015.019

THE FREQUENCY OF ADRENAL INSUFFICIENCY IN ADOLESCENTS AND YOUNG ADULTS WITH THALASSEMIA MAJOR VERSUS THALASSEMIA INTERMEDIA IN IRAN

Sara Matin, Masoud Ghanei Jahromi, Zohreh Karemizadeh, Sezaneh Haghpanah, Vincenzo De Sanctis, Ashraf Soliman, Mehran Karimi
Abstract 1716 | PDF Downloads 775 HTML Downloads 9456

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DOI: https://doi.org/10.4084/mjhid.2015.005

PREVENTION OF ? THALASSEMIA IN NORTHERN ISRAEL - A COST-BENEFIT ANALYSIS.

Ariel Koren, Lora Profeta, Luci Zalman, Haya Palmor, Carina Levin, Ronit Bril Zamir, Stavit Shalev, Orna Blondheim
Abstract 2145 | PDF Downloads 960 HTML Downloads 11566

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DOI: https://doi.org/10.4084/mjhid.2014.012

PREVALENCE OF ALPHA THALASSEMIA IN MICROCYTIC ANEMIA: A TERTIARY CARE EXPERIENCE FROM NORTH INDIA

Monica Sharma, Sanjay Pandey, Ravi Ranjan, Tulika Seth, Renu Saxena
Abstract 1771 | PDF Downloads 1055 HTML Downloads 4381 table Downloads 0 fig 1 Downloads 0 fig 2 Downloads 0

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DOI: https://doi.org/10.4084/mjhid.2015.004

PREVALENCE OF THALASSEMIA AMONG NEWBORNS: A RE-VISITED AFTER 20 YEARS OF A PREVENTION AND CONTROL PROGRAM IN NORTHEAST THAILAND.

Goonnapa Fucharoen
Abstract 1407 | PDF Downloads 833 HTML Downloads 139

Page e2018054

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DOI: https://doi.org/10.4084/mjhid.2018.054

REVIEW AND RECOMMENDATIONS ON MANAGEMENT OF ADULT FEMALE THALASSEMIA PATIE?TS WITH HYPOGONADISM BASED ON LITERATURE REVIEW AND EXPERIENCE OF ICET-A NETWORK SPECIALISTS

Vincenzo De Sanctis
Abstract 5716 | PDF Downloads 1199 HTML Downloads 1850

Page e2017001

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DOI: https://doi.org/10.4084/mjhid.2017.001

DEFERASIROX: OVER A DECADE OF EXPERIENCE IN THALASSEMIA

Ali Taher
Abstract 2215 | PDF Downloads 1342 HTML Downloads 175

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DOI: https://doi.org/10.4084/mjhid.2018.066

THALASSEMIA AND VENOUS THROMBOEMBOLISM

Julien Succar, Khaled M. Musallam, Ali T Taher
Abstract 2597 | PDF Downloads 824 HTML Downloads 4444

Page e2011025

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DOI: https://doi.org/10.4084/mjhid.2011.025

HEMATOPOIETIC STEM CELL TRNSPLANTATION IN THALASSEMIA AND RELATED DISORDERS

Emanuele Angelucci, Federica Pilo, Clara Targhetta, Martina Pettinau, Cristina Depau, Claudia Cogoni, Sara Usai, Mario Pani, Laura Dessì, Donatella Baronciani
Abstract 913 | PDF Downloads 405 HTML Downloads 3879

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HEMATOPOIETIC STEM CELL TRANSPLANTATION IN THALASSEMIA AND SICKLE CELL DISEASE: EXPERIENCE OF MEDITERRANEAN INSTITUTE OF HEMATOLOGY IN A MULTI-ETHNIC POPULATION.

Marco Marziali, Antonella Isgrò, Javid Gaziev, Guido Lucarelli
Abstract 1411 | PDF Downloads 590 HTML Downloads 2861

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INFECTIONS IN THALASSEMIA AND HEMOGLOBINOPATHIES

Bianca Maria Ricerca, Arturo Di Girolamo, Deborah Rund
Abstract 881 | PDF Downloads 495 HTML Downloads 4170

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DETECTION OF ? THALASSEMIA CARRIERS BY RED CELL PARAMETERS OBTAINED FROM AUTOMATIC COUNTERS USING MATHEMATICAL FORMULAS

Idit Lachover Roth, Boaz Lachover, Guy Koren, Carina Levin, Luci Zalman, Ariel Koren
Abstract 4283 | PDF Downloads 1372 HTML Downloads 934

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DOI: https://doi.org/10.4084/mjhid.2018.008

THE EFFECT OF ALPHA THALASSEMIA, HBF and HBC ON HAEMATOLOGICAL PARAMETERS OF SICKLE CELL DISEASE PATIENTS IN IBADAN, NIGERIA.

FASOLA ATINUKE
Abstract 1442 | PDF Downloads 717 HTML Downloads 215

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DOI: https://doi.org/10.4084/MJHID.2022.001

THE ICET-A RECOMMENDATIONS FOR THE DIAGNOSIS AND MANAGEMENT OF DISTURBANCES OF GLUCOSE HOMEOSTASIS IN THALASSEMIA MAJOR PATIENTS

Vincenzo De Sanctis
Abstract 3882 | PDF Downloads 901 HTML Downloads 1055

Page e2016058

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DOI: https://doi.org/10.4084/mjhid.2016.058

EFFECT OF CIS ACTING POTENTIAL REGULATORS IN THE ß GLOBIN GENE CLUSTER ON THE PRODUCTION OF HBF IN THALASSEMIA PATIENTS

Anita Nadkarni
Abstract 891 | PDF Downloads 475 HTML Downloads 3246

Page e2013012

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DOI: https://doi.org/10.4084/mjhid.2013.012

WHAT UNRELATED HEMATOPOIETIC STEM CELL TRANSPLANTATION IN THALASSEMIA TAUGHT US ABOUT TRANSPLANT IMMUNOGENETICS.

Giorgio La Nasa, Adriana Vacca, Roberto Littera, Eugenia Piras, Sandro Orru, Marianna Greco, Carlo Carcassi, Giovanni Caocci
Abstract 2845 | PDF Downloads 947 HTML Downloads 1367 Untitled Downloads 0 Untitled Downloads 0 Untitled Downloads 0

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DOI: https://doi.org/10.4084/mjhid.2016.048

CONCISE REVIEW ON THE FREQUENCY, MAJOR RISK FACTORS AND SURVEILLANCE OF HEPATOCELLULAR CARCINOMA (HCC) IN ?-THALASSEMIAS: PAST, PRESENT AND FUTURE PERSPECTIVES

Vincenzo De Sanctis
Abstract 3700 | PDF Downloads 1316 HTML Downloads 250

Page e2020006

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DOI: https://doi.org/10.4084/mjhid.2020.006

?-THALASSEMIA DISTRIBUTION IN THE OLD WORLD: A HISTORICAL STANDPOINT OF AN ANCIENT DISEASE

Vincenzo De Sanctis
Abstract 9565 | PDF Downloads 3590 HTML Downloads 4137

Page e2017018

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DOI: https://doi.org/10.4084/mjhid.2017.018

EVALUATION OF GLUTATHIONE-S-TRANSFERASE P1 POLYMORPHISM AND ITS RELATION TO BONE MINERAL DENSITY IN EGYPTIAN CHILDREN AND ADOLESCENTS WITH BETA- THALASSEMIA MAJOR

Seham Ragab
Abstract 3674 | PDF Downloads 698 HTML Downloads 2378 Figures Downloads 0

Page e2016004

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DOI: https://doi.org/10.4084/mjhid.2016.004

CARDIAC FUNCTION AND IRON CHELATION IN THALASSEMIA MAJOR AND INTERMEDIA: A REVIEW OF THE UNDERLYING PATHOPHYSIOLOGY AND APPROACH TO CHELATION MANAGEMENT

Athanasios Aessopos, Vasilios Berdoukas
Abstract 1084 | PDF Downloads 386 HTML Downloads 1378

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GENETIC HETEROGENEITY OF BETA GLOBIN MUTATIONS AMONG ASIAN-INDIANS AND IMPORTANCE IN GENETIC COUNSELLING AND DIAGNOSIS

Ravindra Kumar, Kritanjali Singh, Inusha Panigrahi, Sarita Agarwal
Abstract 1490 | PDF Downloads 1076 HTML Downloads 11223 Figure1 Downloads 0 Figure 2 Downloads 0

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DOI: https://doi.org/10.4084/mjhid.2013.003

HEMOGLOBIN ANALYSIS IN THE FIRST YEAR OF LIFE

PEERAPON WONG
Abstract 2883 | PDF Downloads 814 HTML Downloads 2915

Page e2016012

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DOI: https://doi.org/10.4084/mjhid.2016.012

Measurement of erythrocyte lifespan using a CO breath test in patients with thalassemia and the impact of treatment

xiaolin yin, Jingting Luo
Abstract 417 | PDF Downloads 396 HTML Downloads 84

Page e2023050

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DOI: https://doi.org/10.4084/MJHID.2023.050

COAGULOPATHY IN BETA-THALASSEMIA: CURRENT UNDERSTANDING AND FUTURE PERSPECTIVES

M. Domenica Cappellini, Khaled M. Musallam, Alessia Marcon, Ali Taher
Abstract 858 | PDF Downloads 391 HTML Downloads 8003

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The correlation between ineffective erythropoiesis biomarkers and development of extramedullary hematopoiesis in patients with thalassemia

Siriyakorn Chansai, Supawadee Yamsri, Supan Fucharoen, Goonnapa Fucharoen, Nattiya Teawtrakul
Abstract 587 | PDF Downloads 351 HTML Downloads 160

Page e2022052

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DOI: https://doi.org/10.4084/MJHID.2022.052

HEALTH-RELATED QUALITY OF LIFE IN THAI CHILDREN WITH THALASSEMIA AS EVALUATED BY PEDSQL AND EQ-5D-Y: A SINGLE CENTER EXPERIENCE

Pacharapan Surapolchai, Phakatip Sinlapamongkolkul
Abstract 1130 | PDF Downloads 887 HTML Downloads 242

Page e2020036

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DOI: https://doi.org/10.4084/mjhid.2020.036

RECENT INSIGHTS INTO THE POPULATION GENETICS AND DYNAMICS OF THE INHERITED DISORDERS OF HEMOGLOBIN

David J Weatherall
Abstract 864 | PDF Downloads 379 HTML Downloads 447

Page e2009022

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Invasive Pulmonary Aspergillosis in a Sickle Cell Patient Transplant Recipient: A Successful Treatment

Katia Paciaroni, Gioia De Angelis, Cristiano Gallucci, Cecilia Alfieri, Michela Ribersani, Andrea Roveda, Antonella Isgrò, Marco Marziali, Ivan Pietro Aloi, Alessandro Inserra, Javid Gaziev, Pietro Sodani, Guido Lucarelli
Abstract 1662 | PDF Downloads 894 HTML Downloads 1859 Lung computed tomography CT scan image Downloads 0

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DOI: https://doi.org/10.4084/mjhid.2015.006

THE ICET-A SURVEY ON CURRENT CRITERIA USED BY CLINICIANS FOR THE ASSESSMENT OF CENTRAL ADRENAL INSUFFICIENCY IN THALASSEMIA: ANALYSIS OF RESULTS AND RECOMMENDATIONS

Vincenzo De Sanctis
Abstract 3363 | PDF Downloads 645 HTML Downloads 1648

Page e2016034

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DOI: https://doi.org/10.4084/mjhid.2016.034

A MULTICENTER ICET-A SURVEY ON ADHERENCE TO ANNUAL ORAL GLUCOSE TOLERANCE TEST (OGTT) SCREENING IN TRANSFUSION-DEPENDENT THALASSEMIA (TDT) PATIENTS - THE EXPERT CLINICIANS’ OPINION ON FACTORS INFLUENCING THE ADHERENCE AND ON ALTERNATIVE STRATEGIES FOR ADHERENCE OPTIMIZATION

Vincenzo De Sanctis
Abstract 1843 | PDF Downloads 808 HTML Downloads 120

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DOI: https://doi.org/10.4084/MJHID.2025.008

SALIVA IRON AND FERRITIN LEVELS IN PATIENTS WITH THALASSEMIA AND IRON DEFICIENCY ANEMIA

Duran Canatan, Sevgi Kosaci Akdeniz
Abstract 2315 | PDF Downloads 1234 HTML Downloads 10810

Page e2012051

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DOI: https://doi.org/10.4084/mjhid.2012.051

EARLY PREDICTORS OF RENAL DYSFUNCTION IN ?-THALASSEMIA MAJOR AND INTERMEDIA PATIENTS

Azza A.G. Tantawy, Nagham El Bablawy, Amira A. M Adly, Fatma S E Ebeid
Abstract 1651 | PDF Downloads 766 HTML Downloads 3603

Page e2014057

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DOI: https://doi.org/10.4084/mjhid.2014.057

A SEROPREVALENCE OF HBV, HCV AND HIV-1 AND CORRELATION WITH MOLECULAR MARKERS AMONG MULTI-TRANSFUSED THALASSEMIA PATIENTS IN WESTERN INDIA

Kanchan Mishra, Avani Shah, Krima Patel, Kanjaksha Ghosh, Sumit Bharadva
Abstract 969 | PDF Downloads 643 HTML Downloads 218

Page e2020038

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DOI: https://doi.org/10.4084/mjhid.2020.038

THE HISTORY OF DEFERIPRONE (L1) AND THE COMPLETE TREATMENT OF IRON OVERLOAD IN THALASSAEMIA

George J Kontoghiorghes, Marios Kleanthous, Christina N. Kontoghiorghe
Abstract 1887 | PDF Downloads 1355 HTML Downloads 317

Page e2020011

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DOI: https://doi.org/10.4084/mjhid.2020.011

High Prevalence of Antiphospholipid Antibodies in Children with Non-Transfusion Dependent Thalassemia and Possible Correlations with Microparticles

Jitlada Chinsuwan, Phatchanat Klaihmon, Praguywan Kadegasem, Ampaiwan Chuansumrit, Anucha Soisamrong, Kovit Pattanapanyasat, Pakawan Wongwerawattanakoon, Nongnuch Sirachainan
Abstract 563 | PDF Downloads 464 HTML Downloads 204

Page e2020071

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DOI: https://doi.org/10.4084/mjhid.2020.071

CLINICAL AND BIOCHEMICAL DATA OF ADULT THALASSEMIA MAJOR PATIENTS (TM) WITH MULTIPLE ENDOCRINE COMPLICATIONS (MEC) VERSUS TM PATIENTS WITH NORMAL ENDOCRINE FUNCTIONS: A RETROSPECTIVE LONG-TERM STUDY (40 YEARS) IN A TERTIARY CARE CENTER IN ITALY

Vincenzo De Sanctis, Heba Elsedfy
Abstract 3392 | PDF Downloads 814 HTML Downloads 3421

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DOI: https://doi.org/10.4084/mjhid.2016.022

IRON METABOLISM IN THALASSEMIA AND SICKLE CELL DISEASE

Raffaella Mariani, Paola Trombini, Matteo Pozzi, Alberto Piperno
Abstract 1112 | PDF Downloads 493 HTML Downloads 43783

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VITAMIN D STATUS IN THALASSEMIA MAJOR: AN UPDATE

Ashraf Tawfik Soliman
Abstract 1952 | PDF Downloads 893 HTML Downloads 2392

Page e2013057

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DOI: https://doi.org/10.4084/mjhid.2013.057

THALASSAEMIA INTERMEDIA : AN UPDATE

Ali Taher, Khaled M. Musallam, Maria Domenica Cappellini
Abstract 844 | PDF Downloads 364 HTML Downloads 9230

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THERAPEUTIC VALUE OF COMBINED THERAPY WITH DEFERASIROX AND SILYMARIN ON IRON OVERLOAD IN CHILDREN WITH BETA THALASSEMIA

adel abd elhaleim hagag
Abstract 2012 | PDF Downloads 633 HTML Downloads 14843 Therapeutic Value of Combined Therapy with Deferasirox and Silymarin on Iron Overload in Children with Beta Thalassemia Downloads 0

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DOI: https://doi.org/10.4084/mjhid.2013.065

ACQUIRED HYPOGONADOTROPIC HYPOGONADISM (AHH) IN THALASSAEMIA MAJOR PATIENTS: AN UNDERDIAGNOSED CONDITION?

Vincenzo De Sanctis
Abstract 4650 | PDF Downloads 1090 HTML Downloads 3375

Page e2016001

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DOI: https://doi.org/10.4084/mjhid.2016.001

ASSOCIATION OF VDBP RS4701 VARIANT, BUT NOT VDR/RXR-? OVER-EXPRESSION WITH BONE MINERAL DENSITY IN PEDIATRIC ?-THALASSEMIA PATIENTS

Shaimaa Sahmoud, Mostafa S. Ibrahim, Eman A. Toraih, Noha Kamel, Manal Fawzy, Samar Elfiky
Abstract 939 | PDF Downloads 591 HTML Downloads 148

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DOI: https://doi.org/10.4084/mjhid.2020.037

QUANTITATIVE ANALYSIS OF LIVER IRON DEPOSITION BASED ON DUAL-ENERGY CT IN THALASSEMIA PATIENTS

Fengming Xu, Cheng Tang, Yiling Huang, Linlin Liang, Fuling Huang, Gaohui Yang, Peng Peng
Abstract 538 | PDF Downloads 746 HTML Downloads 285

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DOI: https://doi.org/10.4084/MJHID.2023.020

MOLECULAR ANALYSIS OF NON-TRANSFUSION DEPENDENT THALASSEMIA ASSOCIATED WITH HEMOGLOBIN E-?-THALASSEMIA DISEASE WITHOUT ?--THALASSEMIA

Paramee Phanrahan, Supawadee Yamsri, Nattiya Teawtrakul, Goonnapa Fucharoen, Kanokwan Sanchaisuriya, Supan Fucharoen
Abstract 1170 | PDF Downloads 882 HTML Downloads 171

Page e2019038

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DOI: https://doi.org/10.4084/mjhid.2019.038
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eISSN: 2035-3006

Severe Anemia

Vol. 17 No. 1 (2025)

The Mediterranean Journal of Hematology and Infectious Diseases [eISSN 2035-3006]
is owned by the U.C.S.C. and it is published by PAGEPress®, Pavia, Italy.
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