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Editor-in-Chief: Giuseppe Leone | Italy

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  • A MULTICENTER ICET-A SURVEY ON ADHERENCE TO ANNUAL ORAL GLUCOSE TOLERANCE TEST (OGTT) SCREENING IN TRANSFUSION-DEPENDENT THALASSEMIA (TDT) PATIENTS - THE EXPERT CLINICIANS’ OPINION ON FACTORS INFLUENCING THE ADHERENCE AND ON ALTERNATIVE STRATEGIES FOR ADHERENCE OPTIMIZATION Survey on adherence to annual OGTT in thalassemia

    Vincenzo De Sanctis
    e2025008
    2024-12-31
    https://doi.org/10.4084/MJHID.2025.008
    2957
    PDF: 1363
    HTML: 164
  • FINE MAPPING OF GLUCOSE 6 PHOSPHATE DEHYDROGENASE (G6PD) DEFICIENCY IN RURAL AREA OF SOUTH WEST ODISHA USING THE CLINICAL, HEMATOLOGICAL AND MOLECULAR APPROACH

    Ravindra Kumar, MPSS Singh, Soumendu Mahapatra, Sonam Chourasia, Malay Kumar Tripathi, John Oommen, Praveen Kumar Bharti, Rajasubramaniam Shanmugam
    e2020015
    2020-02-26
    https://doi.org/10.4084/mjhid.2020.015
    1789
    PDF: 1045
    HTML: 567
  • Coronavirus disease 2019 (COVID-19) severity in patients with thalassemias: A Nationwide Iranian Experience Coronavirus in patients with thalassemias

    Mehran Karimi, Sezaneh Haghpanah , Azita Azarkeivan , Sara Matin, Arash Safaei, Vincenzo De Sanctis
    e2021008
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.008
    1425
    PDF: 494
    HTML: 187
  • CONCISE REVIEW ON THE FREQUENCY, MAJOR RISK FACTORS AND SURVEILLANCE OF HEPATOCELLULAR CARCINOMA (HCC) IN ?-THALASSEMIAS: PAST, PRESENT AND FUTURE PERSPECTIVES Thalassaemia transfusion dependent, Hepatitis C, hepatocarcinoma.

    Vincenzo De Sanctis
    e2020006
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.006
    4321
    PDF: 1541
    HTML: 462
  • HEMATOPOIETIC STEM CELL TRANSPLANTATION IN THALASSEMIA AND SICKLE CELL DISEASE: EXPERIENCE OF MEDITERRANEAN INSTITUTE OF HEMATOLOGY IN A MULTI-ETHNIC POPULATION.

    Marco Marziali, Antonella Isgrò, Javid Gaziev, Guido Lucarelli
    e2009027
    2009-12-26
    1730
    PDF: 734
    HTML: 2923
  • BACTERIAL INFECTIONS FOLLOWING SPLENECTOMY FOR MALIGNANT AND NONMALIGNANT HEMATOLOGIC DISEASES

    Giuseppe Leone, Eligio Pizzigallo
    e2015057
    2015-10-12
    https://doi.org/10.4084/mjhid.2015.057
    4958
    PDF: 2000
    HTML: 8442
  • FIRST-PHASE INSULIN RESPONSE (FPIR) TO INTRAVENOUS GLUCOSE TOLERANCE TEST (IVGTT), INSULIN SENSITIVITY AND LONG-TERM FOLLOW-UP IN TRANSFUSION-DEPENDENT BETA-THALASSEMIA (TDT) NORMOGLYCEMIC PATIENTS WITH REDUCED INSULIN SECRETION TO ORAL GLUCOSE TOLERANCE TEST: A PILOT STUDY. The function of the endocrine pancreas in transfusion-dependent ?-thalassemia

    Vincenzo De Sanctis
    e2021021
    2021-02-26
    https://doi.org/10.4084/mjhid.2021.021
    7462
    PDF: 578
    HTML: 238
  • PREVALENCE AND AETIOLOGY OF BACTEREMIA IN FEBRILE CHILDREN WITH SICKLE CELL DISEASE AT A NIGERIA TERTIARY HOSPITAL

    Biobele Jotham Brown, Hannah O Dada-Adegbola, Catherine Trippe, Olufunmilayo Olopade
    e2017039
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.039
    3001
    PDF: 1307
    HTML: 1018
  • PREDISPOSING FACTORS TO INFECTIONS IN THALASSEMIA SYNDROME PATIENTS

    Eman M Mansory, Lina M. Abdulrahman, Balsam Osman, Sawsan M. Sawsan, Assil F. Ruckn, Marwa Aljedaani, Nemmat Hassan, Ahmed S. Barefah, Hatem M. Alahwal, Yassir Daghistani, Salem M. Bahashwan, Abdullah T. Almohammadi, Osman O. Radhwi
    e2025055
    2025-08-31
    https://doi.org/10.4084/MJHID.2025.055
    1830
    PDF: 1524
    HTML: 363
  • INFLUENCE OF SICKLE CELL GENE ON THE ALLELIC DIVERSITY AT THE MSP-1 LOCUS OF PLASMODIUM FALCIPARUM IN ADULT PATIENTS WITH SEVERE MALARIA

    Dilip Kumar Patel, Ranjeet Singh Mashon, Prasanta Purohit, Siris Patel, Satyabrata Meher, Snehadhini Dehury, Chhatray Marndi, Kishalaya Das, Bipin Kishore Kullu, Padmalaya Das
    e2015050
    2015-08-24
    https://doi.org/10.4084/mjhid.2015.050
    1573
    PDF: 891
    HTML: 6366
  • PREVALENCE OF ß-THALASSEMIA MUTATIONS AMONG NORTHEASTERN IRANIAN POPULATION AND THEIR IMPACTS ON HEMATOLOGICAL INDICES AND APPLICATION OF PRENATAL DIAGNOSIS, A SEVEN-YEARS STUDY

    Mohammad Ehsan Jaripour, Kourosh Hayatigolkhatmi, Vahid Iranmanesh, Farhad Khadivi Zand, Zahra Badiei, Hamid Farhangi, Ali Ghasemi, Abdollah Banihashem, Reza Jafarzadeh Esfehani, Ariane Sadr-Nabavi
    e2018042
    2018-07-01
    https://doi.org/10.4084/mjhid.2018.042
    2447
    PDF: 979
    HTML: 401
    Supplementary table 1: 230
    Some of the mutation detection samples: 221
  • GENETIC HETEROGENEITY OF BETA GLOBIN MUTATIONS AMONG ASIAN-INDIANS AND IMPORTANCE IN GENETIC COUNSELLING AND DIAGNOSIS

    Ravindra Kumar, Kritanjali Singh, Inusha Panigrahi, Sarita Agarwal
    e2013003
    2013-01-01
    https://doi.org/10.4084/mjhid.2013.003
    1797
    PDF: 1307
    HTML: 11527
    Figure1: 182
    Figure 2: 185
  • ASSOCİATİON BETWEEN IRON OVERLOAD AND GLUCOSE METABOLİSM İN CHİLDREN AND YOUTH WİTH TRANSFUSİON-DEPENDENT BETA THALASSEMİA: THE ROLE OF CHELATİON THERAPY

    Deniz Guven, Dr. İncefidan, Dr. Kazanci, Dr. Ozlem Kara
    2026-02-28
    https://doi.org/10.4084/MJHID.2026.017
    693
    PDF: 595
    HTML: 77
  • PATIENTS WITH HAEMOGLOBINOPATHIES AND CHRONIC HEPATITIS C: A REALLY DIFFICULT TO TREAT POPULATION IN 2016?

    Kalliopi Zachou, Pinelopi Arvaniti, Nikolaos K. Gatselis, Kalliopi Azariadis, Georgia Papadamou, Eirini Rigopoulou, George N. Dalekos
    e2017003
    2017-01-01
    https://doi.org/10.4084/mjhid.2017.003
    2971
    PDF: 997
    HTML: 2068
    Cover letter: 187
  • How we prevented an anti-P1 mediated hemolytic transfusion reaction

    Beatrice Borsellino, Tiziano Martini, Rino Biguzzi, Irene Francesconi, Maria Federica Currà, Sabrina Lelli
    e2024009
    2024-01-01
    https://doi.org/10.4084/MJHID.2024.009
    1200
    PDF: 1243
    HTML: 339
  • PREVALENCE OF HEPATITIS B, HEPATITIS C AND HIV IN MULTIPLY TRANSFUSED SICKLE CELL DISEASE PATIENTS FROM OMAN HBV,HCV and HIV and Sickle Cell Disease.

    Anil Pathare, Salam Alkindi, prof.
    e2019058
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.058
    1680
    PDF: 1022
    HTML: 374
  • REDUCTION OF INTRAMEDULLARY APOPTOSIS AFTER STEM CELL TRANSPLANTATION IN BLACK AFRICAN VARIANT OF PEDIATRIC SICKLE CELL ANEMIA.

    Antonella Isgrò, Pietro Sodani, Marco Marziali, Javid Gaziev, Daniela Fraboni, Katia Paciaroni, Cristiano Gallucci, Gioia De Angelis, Cecilia Alfieri, Michela Ribersani, Daniele Armiento, Andrea Roveda, Marco Andreani, Manuela Testi, Guido Lucarelli
    e2014054
    2014-07-06
    https://doi.org/10.4084/mjhid.2014.054
    2470
    PDF: 1132
    HTML: 2121
  • THE START-UP OF THE FIRST HEMATOPOIETIC STEM CELL TRANSPLANTATION CENTER IN THE IRAQI KURDISTAN: A CAPACITY-BUILDING COOPERATIVE PROJECT BY THE HIWA CANCER HOSPITAL, SULAYMANIYAH, AND THE ITALIAN AGENCY FOR DEVELOPMENT COOPERATION

    Ignazio Majolino
    e2017031
    2017-04-15
    https://doi.org/10.4084/mjhid.2017.031
    2418
    PDF: 1031
    HTML: 2086
  • HEMATOPOIETIC STEM CELL TRANSPLANTATION IN SEVERE PEDIATRIC SICKLE CELL DISEASE: OUTCOME AND LONG-TERM COMPLICATIONS, SAUDI EXPERIENCE AT KING FAISAL SPECIALIST HOSPITAL, RIYADH, SAUDI ARABIA HCT in in Severe Pediatric Sickle Cell Disease

    Abdullah Al-Jefri, Fatema Al-Hashem, Khawar, Amal Al-Seraihy, Ali Al-Ahmari, Ibrahim Ghemlas, Awatif AlAnazi, Hawazen Al-Saedi, Saadiya Khan, Abdulrahman Al-Musa, Mahasen Saleh, Mouhab Ayas
    e2025030
    2025-04-30
    https://doi.org/10.4084/MJHID.2025.030
    1306
    PDF: 965
    HTML: 471
  • HEMATOPOIETIC STEM CELL TRANSPLANTATION IN EGYPT CHALLENGES AND OPPORTUNITIES

    Hossam Kamel Mahmoud, Gamaleldin Mohamed Fathy, Alaa Elhaddad, Omar Abdelrahman Fahmy, Mohamed Abdelmooti, Raafat Abdelfattah, Mahmoud Tarek Sayed Ahmed Bokhary
    e2020023
    2020-04-27
    https://doi.org/10.4084/mjhid.2020.023
    1899
    PDF: 998
    HTML: 793
  • Invasive Pulmonary Aspergillosis in a Sickle Cell Patient Transplant Recipient: A Successful Treatment

    Katia Paciaroni, Gioia De Angelis, Cristiano Gallucci, Cecilia Alfieri, Michela Ribersani, Andrea Roveda, Antonella Isgrò, Marco Marziali, Ivan Pietro Aloi, Alessandro Inserra, Javid Gaziev, Pietro Sodani, Guido Lucarelli
    e2015006
    2015-08-01
    https://doi.org/10.4084/mjhid.2015.006
    1972
    PDF: 1129
    HTML: 1902
    Lung computed tomography CT scan image: 212
  • Formulas for the Detection ?-Thalassemia Carriers Are Affected by Changes in Red Cell Parameters

    Deniz Aslan
    e2018026
    2018-04-20
    https://doi.org/10.4084/mjhid.2018.026
    1384
    PDF: 689
    HTML: 354
  • Concordance Rate of Fasting Plasma Glucose (PG) and 2-hour PG post Oral Glucose Tolerance Test (OGTT) in Patients with new diagnosis of Thalassemia-Related Diabetes Mellitus (Th-RDM):Implications for Clinical Practice OGTT concordance rate in thalassemia major

    Vincenzo De Sanctis, Mohammad Faranoush, Shahina Daar, Ihab Elhakim, Ashraf T Soliman, Forough Saki, Mehran Karimi, Ploutarchos Tzoulis
    e2026011
    2026-01-01
    https://doi.org/10.4084/MJHID.2026.011
    699
    PDF: 540
    Html: 119
  • Hyperhemolytic Syndrome complicating a Delayed Hemolytic Transfusion Reaction due to anti-P1 alloimmunization, in a pregnant woman with HbO-Arab?-thalassemia

    Zoe Bezirgiannidou, Anna Christoforidou, Eftychia Kontekaki, Athanasios Anastasiadis, Spyros Papamichos, Helen Menexidou, Dimitrios Margaritis, George Martinis, Elpidoforos Mandadakis
    e2016053
    2016-10-18
    https://doi.org/10.4084/mjhid.2016.053
    3225
    PDF: 926
    HTML: 1283
    Figure 1: 172
  • SURVIVAL PROBABILITY IN PATIENTS WITH SICKLE CELL ANEMIA USING THE COMPETITIVE RISK STATISTICAL MODEL

    Samir Ballas, Emilia Matos do Nascimento, PhD, Clarisse Lopes de Castro Lobo, MD, Basilio de Bragança Pereira, PhD
    e2019022
    2019-02-26
    https://doi.org/10.4084/mjhid.2019.022
    1567
    PDF: 958
    HTML: 216
  • LIVER IRON CONTENT (LIC) IN ADULTS WITH NON-TRANSFUSION DEPENDENT SICKLE CELL DISEASE (NT-SCD). CORRELATION WITH SERUM FERRITIN AND LIVER ENZYMES CONCENTRATIONS

    Vincenzo De Sanctis
    e2017037
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.037
    3970
    PDF: 997
    HTML: 1155
  • Elevated endogenous alveolar carbon monoxide concentration in patients with transfusion-dependent thalassemia and its relation to ineffective erythropoiesis

    Yanni Xie
    e2025047
    2025-06-29
    https://doi.org/10.4084/MJHID.2025.047
    599
    PDF: 455
    HTML: 41
  • THE HISTORY OF DEFERIPRONE (L1) AND THE COMPLETE TREATMENT OF IRON OVERLOAD IN THALASSAEMIA The history and roles of deferiprone

    George J Kontoghiorghes, Marios Kleanthous, Christina N. Kontoghiorghe
    e2020011
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.011
    2467
    PDF: 1613
    HTML: 662
  • PREVALENCE OF ALPHA THALASSEMIA IN MICROCYTIC ANEMIA: A TERTIARY CARE EXPERIENCE FROM NORTH INDIA

    Monica Sharma, Sanjay Pandey, Ravi Ranjan, Tulika Seth, Renu Saxena
    e2015004
    2015-01-01
    https://doi.org/10.4084/mjhid.2015.004
    2477
    PDF: 1247
    HTML: 4756
    table: 217
    fig 1: 231
    fig 2: 184
  • PERIOPERATIVE MANAGEMENT OF SICKLE CELL DISEASE: A NARRATIVE REVIEW

    Kwame Ofori Adjepong, Folashade Otegbeye, Yaw Amoateng ADJEPONG
    e2018032
    2018-05-01
    https://doi.org/10.4084/mjhid.2018.032
    8759
    PDF: 3278
    HTML: 1408
  • THE ICET-A RECOMMENDATIONS FOR THE DIAGNOSIS AND MANAGEMENT OF DISTURBANCES OF GLUCOSE HOMEOSTASIS IN THALASSEMIA MAJOR PATIENTS

    Vincenzo De Sanctis
    e2016058
    2016-10-25
    https://doi.org/10.4084/mjhid.2016.058
    4272
    PDF: 1232
    HTML: 1216
  • RECENT INSIGHTS INTO THE POPULATION GENETICS AND DYNAMICS OF THE INHERITED DISORDERS OF HEMOGLOBIN

    David J Weatherall
    e2009022
    2009-12-20
    1066
    PDF: 458
    HTML: 586
  • THE USE OF HPLC AS A TOOL FOR NEONATAL CORD BLOOD SCREENING OF HAEMOGLOBINOPATHY - A VALIDATION STUDY

    A. Al-Madhani, Anil Pathare, Salam Alkindi
    e2019005
    2019-01-01
    https://doi.org/10.4084/mjhid.2019.005
    2073
    PDF: 1213
    HTML: 377
  • Thalassemia carrier detection among pregnant women Thalassemia carrier detection among pregnant women

    Edhyana Sahiratmadja, Merry M.V. Seu, Ita M. Nainggolan, Johanes C. Mose, Ramdan Panigoro
    e2021003
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.003
    1979
    PDF: 668
    HTML: 264
  • COAGULOPATHY IN BETA-THALASSEMIA: CURRENT UNDERSTANDING AND FUTURE PERSPECTIVES

    M. Domenica Cappellini, Khaled M. Musallam, Alessia Marcon, Ali Taher
    e2009029
    2009-12-28
    1197
    PDF: 492
    HTML: 8189
  • DETECTION OF ? THALASSEMIA CARRIERS BY RED CELL PARAMETERS OBTAINED FROM AUTOMATIC COUNTERS USING MATHEMATICAL FORMULAS

    Idit Lachover Roth, Boaz Lachover, Guy Koren, Carina Levin, Luci Zalman, Ariel Koren
    e2018008
    2018-01-01
    https://doi.org/10.4084/mjhid.2018.008
    4912
    PDF: 1744
    HTML: 1111
  • CEREBRAL VENOUS THROMBOSIS IN THE MEDITERRANEAN AREA IN CHILDREN

    S Menascu, A Lotan, B Ben Zeev, U Nowak- Gottl, G Kenet
    e2011029
    2011-07-08
    https://doi.org/10.4084/mjhid.2011.029
    2540
    PDF: 969
    HTML: 2245
  • A MULTICENTER ICET-A STUDY ON AGE AT MENARCHE AND MENSTRUAL CYCLES IN PATIENTS WITH TRANSFUSION-DEPENDENT THALASSEMIA (TDT) WHO STARTED EARLY CHELATION THERAPY WITH DIFFERENT CHELATING AGENTS. Age at menarche and menstrual cycles in patients with transfusion-dependent thalassemia.

    SALVATORE DI MAIO, VINCENZO DE SANCTIS, PIERLUIGI MARZUILLO, CHRISTOS KATTAMIS, SHAHINA DAAR, MEHERAN KARIMI, SAKI FOROUGH, ATANAS BANKEV, VALERIA KALEVA, SOTEROULA CHRISTOU, CARMELO FORTUGNO, POLYXENI DELAPORTA, ASHRAF T SOLIMAN , PLOUTARCHOS TZOULIS
    e2023058
    2023-10-30
    https://doi.org/10.4084/MJHID.2023.058
    820
    PDF: 540
    HTML: 121
  • Phenotyping of Rh, Kell, Duffy and Kidd blood group antigens among non-tribal and tribal population of South Gujarat and its implication in preventing alloimmunisations in multitransfused patients.

    Avani Shah, Kanjaksha Ghosh, Preeti Sharma, Kanchan Mishra
    e2018070
    2018-10-30
    https://doi.org/10.4084/mjhid.2018.070
    1929
    PDF: 913
    HTML: 601
  • CARDIAC FUNCTION AND IRON CHELATION IN THALASSEMIA MAJOR AND INTERMEDIA: A REVIEW OF THE UNDERLYING PATHOPHYSIOLOGY AND APPROACH TO CHELATION MANAGEMENT

    Athanasios Aessopos, Vasilios Berdoukas
    e2009002
    2009-07-18
    1618
    PDF: 489
    HTML: 1449
  • EFFECTS OF THALIDOMIDE ON ENDOTHELIAL ACTIVATION AND STRESS INDEX IN CHILDREN WITH Β-THALASSEMIA MAJOR

    Kun Yang
    e2024076
    2024-10-31
    https://doi.org/10.4084/MJHID.2024.076
    1081
    PDF: 598
    HTML: 153
  • CHARACTERIZATION AND ANTIMICROBIAL SUSCEPTIBILITY PROFILE OF SEPTICAEMIA-CAUSING PATHOGENS ISOLATED FROM FEBRILE CHILDREN WITH SICKLE CELL DISEASE IN KANO, NIGERIA.

    Ibrahim Yusuf
    e2018016
    2018-02-15
    https://doi.org/10.4084/mjhid.2018.016
    2917
    PDF: 999
    HTML: 527
  • Luspatercept Treatment in a β-Thalassemia Patient with Pulmonary Arterial Hypertension: A Case Report

    beibei yang, dongmei liu, changyu yang, Yali zhou, Guiping Liao, jian huang, Yingying Li, yinjiang tang, xiaolin yin
    e2025059
    2025-08-31
    https://doi.org/10.4084/MJHID.2025.059
    1171
    PDF: 577
    Html: 158
  • The EVOLVING ROLE OF HAEMATOLOGY NURSING PRACTICE: A CROSS-SECTIONAL SURVEY

    Sarah Liptrott, Mairéad NíChonghaile, Liz O'Connell, Erik Aerts
    e2023033
    2023-04-28
    https://doi.org/10.4084/MJHID.2023.033
    1951
    Suppl. Files: 901
    HTML: 440
    PDF: 761
  • Clinical and laboratory features of Hemoglobin La Desirade variant in association with sickle cell and alpha thalassemia genes Clinical & laboratory features of Hb La Desirade trait and compound heterozygous for Hb La Desirade and HbS Hemoglobin.

    Salam Alkindi, Shoaib Al Zadjali, Mohamed Al Rawahi , Hamoud Al Haddabi, Shahina Daar, Refaat Abdullah Elsadek, Bahaa Eldeen Diab Sherkawy, Anil Pathare
    e2021010
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.010
    1755
    PDF: 485
    HTML: 260
  • IRON CHELATION THERAPY IN THALASSEMIA SYNDROMES

    Paolo Cianciulli
    e2009034
    1304
    PDF: 629
    HTML: 2325
  • HB H DISEASE CAUSED BY UNIPARENTAL DISOMY: FIRST REPORT OF THE αT-SAUDIΑ MUTATION IN THE CHINESE POPULATION

    Ge Wang, Hongting Xie, Jun Zhang, Peng Huang, Min Liang, Dina Zhu, Qianqian Zhang, Yuqiu Zhou, Xuan Shang
    e2024069
    2024-08-31
    https://doi.org/10.4084/MJHID.2024.069
    1046
    PDF: 620
    Html: 126
    Suppl. Files: 452
  • A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β⁺-Thalassaemia Patient

    Marta Bortolotti, Gianluca Costamagna, Marta Mancarella, Delia Gagliardi, Silvia Lanfranconi, Alessia Marcon, Margherita Migone De Amicis, Nereo Bresolin, Stefania Corti, Giovanna Graziadei
    e2022019
    2022-02-27
    https://doi.org/10.4084/MJHID.2022.019
    1022
    PDF: 567
    HTML: 251
  • Clinical spectrum and genotypes of children with alpha-thalassemia in northeastern, Thailand

    Patcharee Komvilaisak, Nattakarn Sangkha, Arunee Jetsrisuparp, Kunanya Suwannaying, Goonnapa Fucharoen, Napat Laoaroon
    e2025081
    2025-10-31
    https://doi.org/10.4084/MJHID.2025.081
    332
    PDF: 233
    Html: 83
  • ASSOCIATION OF VDBP RS4701 VARIANT, BUT NOT VDR/RXR-? OVER-EXPRESSION WITH BONE MINERAL DENSITY IN PEDIATRIC ?-THALASSEMIA PATIENTS Vitamin D metabolic axis and BMD in ?-thalassemia

    Shaimaa Sahmoud, Mostafa S. Ibrahim, Eman A. Toraih, Noha Kamel, Manal Fawzy, Samar Elfiky
    e2020037
    2020-06-28
    https://doi.org/10.4084/mjhid.2020.037
    1302
    PDF: 748
    HTML: 213
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