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Editor-in-Chief: Giuseppe Leone | Italy

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  • A MULTICENTER ICET-A SURVEY ON ADHERENCE TO ANNUAL ORAL GLUCOSE TOLERANCE TEST (OGTT) SCREENING IN TRANSFUSION-DEPENDENT THALASSEMIA (TDT) PATIENTS - THE EXPERT CLINICIANS’ OPINION ON FACTORS INFLUENCING THE ADHERENCE AND ON ALTERNATIVE STRATEGIES FOR ADHERENCE OPTIMIZATION Survey on adherence to annual OGTT in thalassemia

    Vincenzo De Sanctis
    e2025008
    2024-12-31
    https://doi.org/10.4084/MJHID.2025.008
    2931
    PDF: 1347
    HTML: 159
  • FINE MAPPING OF GLUCOSE 6 PHOSPHATE DEHYDROGENASE (G6PD) DEFICIENCY IN RURAL AREA OF SOUTH WEST ODISHA USING THE CLINICAL, HEMATOLOGICAL AND MOLECULAR APPROACH

    Ravindra Kumar, MPSS Singh, Soumendu Mahapatra, Sonam Chourasia, Malay Kumar Tripathi, John Oommen, Praveen Kumar Bharti, Rajasubramaniam Shanmugam
    e2020015
    2020-02-26
    https://doi.org/10.4084/mjhid.2020.015
    1767
    PDF: 1033
    HTML: 549
  • Coronavirus disease 2019 (COVID-19) severity in patients with thalassemias: A Nationwide Iranian Experience Coronavirus in patients with thalassemias

    Mehran Karimi, Sezaneh Haghpanah , Azita Azarkeivan , Sara Matin, Arash Safaei, Vincenzo De Sanctis
    e2021008
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.008
    1373
    PDF: 476
    HTML: 182
  • CONCISE REVIEW ON THE FREQUENCY, MAJOR RISK FACTORS AND SURVEILLANCE OF HEPATOCELLULAR CARCINOMA (HCC) IN ?-THALASSEMIAS: PAST, PRESENT AND FUTURE PERSPECTIVES Thalassaemia transfusion dependent, Hepatitis C, hepatocarcinoma.

    Vincenzo De Sanctis
    e2020006
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.006
    4290
    PDF: 1525
    HTML: 458
  • HEMATOPOIETIC STEM CELL TRANSPLANTATION IN THALASSEMIA AND SICKLE CELL DISEASE: EXPERIENCE OF MEDITERRANEAN INSTITUTE OF HEMATOLOGY IN A MULTI-ETHNIC POPULATION.

    Marco Marziali, Antonella Isgrò, Javid Gaziev, Guido Lucarelli
    e2009027
    2009-12-26
    1694
    PDF: 723
    HTML: 2922
  • BACTERIAL INFECTIONS FOLLOWING SPLENECTOMY FOR MALIGNANT AND NONMALIGNANT HEMATOLOGIC DISEASES

    Giuseppe Leone, Eligio Pizzigallo
    e2015057
    2015-10-12
    https://doi.org/10.4084/mjhid.2015.057
    4901
    PDF: 1981
    HTML: 8408
  • FIRST-PHASE INSULIN RESPONSE (FPIR) TO INTRAVENOUS GLUCOSE TOLERANCE TEST (IVGTT), INSULIN SENSITIVITY AND LONG-TERM FOLLOW-UP IN TRANSFUSION-DEPENDENT BETA-THALASSEMIA (TDT) NORMOGLYCEMIC PATIENTS WITH REDUCED INSULIN SECRETION TO ORAL GLUCOSE TOLERANCE TEST: A PILOT STUDY. The function of the endocrine pancreas in transfusion-dependent ?-thalassemia

    Vincenzo De Sanctis
    e2021021
    2021-02-26
    https://doi.org/10.4084/mjhid.2021.021
    7370
    PDF: 566
    HTML: 236
  • ASSOCİATİON BETWEEN IRON OVERLOAD AND GLUCOSE METABOLİSM İN CHİLDREN AND YOUTH WİTH TRANSFUSİON-DEPENDENT BETA THALASSEMİA: THE ROLE OF CHELATİON THERAPY

    Deniz Guven, Dr. İncefidan, Dr. Kazanci, Dr. Ozlem Kara
    2026-02-28
    https://doi.org/10.4084/MJHID.2026.017
    660
    PDF: 549
    HTML: 72
  • PATIENTS WITH HAEMOGLOBINOPATHIES AND CHRONIC HEPATITIS C: A REALLY DIFFICULT TO TREAT POPULATION IN 2016?

    Kalliopi Zachou, Pinelopi Arvaniti, Nikolaos K. Gatselis, Kalliopi Azariadis, Georgia Papadamou, Eirini Rigopoulou, George N. Dalekos
    e2017003
    2017-01-01
    https://doi.org/10.4084/mjhid.2017.003
    2950
    PDF: 984
    HTML: 2065
    Cover letter: 181
  • How we prevented an anti-P1 mediated hemolytic transfusion reaction

    Beatrice Borsellino, Tiziano Martini, Rino Biguzzi, Irene Francesconi, Maria Federica Currà, Sabrina Lelli
    e2024009
    2024-01-01
    https://doi.org/10.4084/MJHID.2024.009
    1166
    PDF: 1223
    HTML: 258
  • PREVALENCE OF HEPATITIS B, HEPATITIS C AND HIV IN MULTIPLY TRANSFUSED SICKLE CELL DISEASE PATIENTS FROM OMAN HBV,HCV and HIV and Sickle Cell Disease.

    Anil Pathare, Salam Alkindi, prof.
    e2019058
    2019-10-30
    https://doi.org/10.4084/mjhid.2019.058
    1645
    PDF: 1002
    HTML: 367
  • REDUCTION OF INTRAMEDULLARY APOPTOSIS AFTER STEM CELL TRANSPLANTATION IN BLACK AFRICAN VARIANT OF PEDIATRIC SICKLE CELL ANEMIA.

    Antonella Isgrò, Pietro Sodani, Marco Marziali, Javid Gaziev, Daniela Fraboni, Katia Paciaroni, Cristiano Gallucci, Gioia De Angelis, Cecilia Alfieri, Michela Ribersani, Daniele Armiento, Andrea Roveda, Marco Andreani, Manuela Testi, Guido Lucarelli
    e2014054
    2014-07-06
    https://doi.org/10.4084/mjhid.2014.054
    2448
    PDF: 1120
    HTML: 2115
  • THE START-UP OF THE FIRST HEMATOPOIETIC STEM CELL TRANSPLANTATION CENTER IN THE IRAQI KURDISTAN: A CAPACITY-BUILDING COOPERATIVE PROJECT BY THE HIWA CANCER HOSPITAL, SULAYMANIYAH, AND THE ITALIAN AGENCY FOR DEVELOPMENT COOPERATION

    Ignazio Majolino
    e2017031
    2017-04-15
    https://doi.org/10.4084/mjhid.2017.031
    2291
    PDF: 1017
    HTML: 2081
  • HEMATOPOIETIC STEM CELL TRANSPLANTATION IN SEVERE PEDIATRIC SICKLE CELL DISEASE: OUTCOME AND LONG-TERM COMPLICATIONS, SAUDI EXPERIENCE AT KING FAISAL SPECIALIST HOSPITAL, RIYADH, SAUDI ARABIA HCT in in Severe Pediatric Sickle Cell Disease

    Abdullah Al-Jefri, Fatema Al-Hashem, Khawar, Amal Al-Seraihy, Ali Al-Ahmari, Ibrahim Ghemlas, Awatif AlAnazi, Hawazen Al-Saedi, Saadiya Khan, Abdulrahman Al-Musa, Mahasen Saleh, Mouhab Ayas
    e2025030
    2025-04-30
    https://doi.org/10.4084/MJHID.2025.030
    1204
    PDF: 949
    HTML: 457
  • HEMATOPOIETIC STEM CELL TRANSPLANTATION IN EGYPT CHALLENGES AND OPPORTUNITIES

    Hossam Kamel Mahmoud, Gamaleldin Mohamed Fathy, Alaa Elhaddad, Omar Abdelrahman Fahmy, Mohamed Abdelmooti, Raafat Abdelfattah, Mahmoud Tarek Sayed Ahmed Bokhary
    e2020023
    2020-04-27
    https://doi.org/10.4084/mjhid.2020.023
    1851
    PDF: 990
    HTML: 715
  • Invasive Pulmonary Aspergillosis in a Sickle Cell Patient Transplant Recipient: A Successful Treatment

    Katia Paciaroni, Gioia De Angelis, Cristiano Gallucci, Cecilia Alfieri, Michela Ribersani, Andrea Roveda, Antonella Isgrò, Marco Marziali, Ivan Pietro Aloi, Alessandro Inserra, Javid Gaziev, Pietro Sodani, Guido Lucarelli
    e2015006
    2015-08-01
    https://doi.org/10.4084/mjhid.2015.006
    1947
    PDF: 1106
    HTML: 1898
    Lung computed tomography CT scan image: 205
  • Formulas for the Detection ?-Thalassemia Carriers Are Affected by Changes in Red Cell Parameters

    Deniz Aslan
    e2018026
    2018-04-20
    https://doi.org/10.4084/mjhid.2018.026
    1368
    PDF: 670
    HTML: 320
  • Concordance Rate of Fasting Plasma Glucose (PG) and 2-hour PG post Oral Glucose Tolerance Test (OGTT) in Patients with new diagnosis of Thalassemia-Related Diabetes Mellitus (Th-RDM):Implications for Clinical Practice OGTT concordance rate in thalassemia major

    Vincenzo De Sanctis, Mohammad Faranoush, Shahina Daar, Ihab Elhakim, Ashraf T Soliman, Forough Saki, Mehran Karimi, Ploutarchos Tzoulis
    e2026011
    2026-01-01
    https://doi.org/10.4084/MJHID.2026.011
    635
    PDF: 512
    Html: 109
  • Hyperhemolytic Syndrome complicating a Delayed Hemolytic Transfusion Reaction due to anti-P1 alloimmunization, in a pregnant woman with HbO-Arab?-thalassemia

    Zoe Bezirgiannidou, Anna Christoforidou, Eftychia Kontekaki, Athanasios Anastasiadis, Spyros Papamichos, Helen Menexidou, Dimitrios Margaritis, George Martinis, Elpidoforos Mandadakis
    e2016053
    2016-10-18
    https://doi.org/10.4084/mjhid.2016.053
    3206
    PDF: 903
    HTML: 1276
    Figure 1: 160
  • SURVIVAL PROBABILITY IN PATIENTS WITH SICKLE CELL ANEMIA USING THE COMPETITIVE RISK STATISTICAL MODEL

    Samir Ballas, Emilia Matos do Nascimento, PhD, Clarisse Lopes de Castro Lobo, MD, Basilio de Bragança Pereira, PhD
    e2019022
    2019-02-26
    https://doi.org/10.4084/mjhid.2019.022
    1541
    PDF: 943
    HTML: 213
  • LIVER IRON CONTENT (LIC) IN ADULTS WITH NON-TRANSFUSION DEPENDENT SICKLE CELL DISEASE (NT-SCD). CORRELATION WITH SERUM FERRITIN AND LIVER ENZYMES CONCENTRATIONS

    Vincenzo De Sanctis
    e2017037
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.037
    3897
    PDF: 980
    HTML: 1152
  • Elevated endogenous alveolar carbon monoxide concentration in patients with transfusion-dependent thalassemia and its relation to ineffective erythropoiesis

    Yanni Xie
    e2025047
    2025-06-29
    https://doi.org/10.4084/MJHID.2025.047
    588
    PDF: 448
    HTML: 37
  • THE HISTORY OF DEFERIPRONE (L1) AND THE COMPLETE TREATMENT OF IRON OVERLOAD IN THALASSAEMIA The history and roles of deferiprone

    George J Kontoghiorghes, Marios Kleanthous, Christina N. Kontoghiorghe
    e2020011
    2020-01-01
    https://doi.org/10.4084/mjhid.2020.011
    2423
    PDF: 1594
    HTML: 642
  • PREVALENCE OF ALPHA THALASSEMIA IN MICROCYTIC ANEMIA: A TERTIARY CARE EXPERIENCE FROM NORTH INDIA

    Monica Sharma, Sanjay Pandey, Ravi Ranjan, Tulika Seth, Renu Saxena
    e2015004
    2015-01-01
    https://doi.org/10.4084/mjhid.2015.004
    2436
    PDF: 1233
    HTML: 4718
    table: 209
    fig 1: 221
    fig 2: 178
  • PERIOPERATIVE MANAGEMENT OF SICKLE CELL DISEASE: A NARRATIVE REVIEW

    Kwame Ofori Adjepong, Folashade Otegbeye, Yaw Amoateng ADJEPONG
    e2018032
    2018-05-01
    https://doi.org/10.4084/mjhid.2018.032
    8422
    PDF: 3252
    HTML: 1240
  • THE ICET-A RECOMMENDATIONS FOR THE DIAGNOSIS AND MANAGEMENT OF DISTURBANCES OF GLUCOSE HOMEOSTASIS IN THALASSEMIA MAJOR PATIENTS

    Vincenzo De Sanctis
    e2016058
    2016-10-25
    https://doi.org/10.4084/mjhid.2016.058
    4246
    PDF: 1216
    HTML: 1203
  • RECENT INSIGHTS INTO THE POPULATION GENETICS AND DYNAMICS OF THE INHERITED DISORDERS OF HEMOGLOBIN

    David J Weatherall
    e2009022
    2009-12-20
    1057
    PDF: 451
    HTML: 583
  • THE USE OF HPLC AS A TOOL FOR NEONATAL CORD BLOOD SCREENING OF HAEMOGLOBINOPATHY - A VALIDATION STUDY

    A. Al-Madhani, Anil Pathare, Salam Alkindi
    e2019005
    2019-01-01
    https://doi.org/10.4084/mjhid.2019.005
    2008
    PDF: 1196
    HTML: 374
  • Thalassemia carrier detection among pregnant women Thalassemia carrier detection among pregnant women

    Edhyana Sahiratmadja, Merry M.V. Seu, Ita M. Nainggolan, Johanes C. Mose, Ramdan Panigoro
    e2021003
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.003
    1900
    PDF: 654
    HTML: 252
  • COAGULOPATHY IN BETA-THALASSEMIA: CURRENT UNDERSTANDING AND FUTURE PERSPECTIVES

    M. Domenica Cappellini, Khaled M. Musallam, Alessia Marcon, Ali Taher
    e2009029
    2009-12-28
    1125
    PDF: 487
    HTML: 8178
  • DETECTION OF ? THALASSEMIA CARRIERS BY RED CELL PARAMETERS OBTAINED FROM AUTOMATIC COUNTERS USING MATHEMATICAL FORMULAS

    Idit Lachover Roth, Boaz Lachover, Guy Koren, Carina Levin, Luci Zalman, Ariel Koren
    e2018008
    2018-01-01
    https://doi.org/10.4084/mjhid.2018.008
    4864
    PDF: 1722
    HTML: 1105
  • CEREBRAL VENOUS THROMBOSIS IN THE MEDITERRANEAN AREA IN CHILDREN

    S Menascu, A Lotan, B Ben Zeev, U Nowak- Gottl, G Kenet
    e2011029
    2011-07-08
    https://doi.org/10.4084/mjhid.2011.029
    2523
    PDF: 953
    HTML: 2236
  • A MULTICENTER ICET-A STUDY ON AGE AT MENARCHE AND MENSTRUAL CYCLES IN PATIENTS WITH TRANSFUSION-DEPENDENT THALASSEMIA (TDT) WHO STARTED EARLY CHELATION THERAPY WITH DIFFERENT CHELATING AGENTS. Age at menarche and menstrual cycles in patients with transfusion-dependent thalassemia.

    SALVATORE DI MAIO, VINCENZO DE SANCTIS, PIERLUIGI MARZUILLO, CHRISTOS KATTAMIS, SHAHINA DAAR, MEHERAN KARIMI, SAKI FOROUGH, ATANAS BANKEV, VALERIA KALEVA, SOTEROULA CHRISTOU, CARMELO FORTUGNO, POLYXENI DELAPORTA, ASHRAF T SOLIMAN , PLOUTARCHOS TZOULIS
    e2023058
    2023-10-30
    https://doi.org/10.4084/MJHID.2023.058
    797
    PDF: 511
    HTML: 118
  • Phenotyping of Rh, Kell, Duffy and Kidd blood group antigens among non-tribal and tribal population of South Gujarat and its implication in preventing alloimmunisations in multitransfused patients.

    Avani Shah, Kanjaksha Ghosh, Preeti Sharma, Kanchan Mishra
    e2018070
    2018-10-30
    https://doi.org/10.4084/mjhid.2018.070
    1878
    PDF: 897
    HTML: 591
  • CARDIAC FUNCTION AND IRON CHELATION IN THALASSEMIA MAJOR AND INTERMEDIA: A REVIEW OF THE UNDERLYING PATHOPHYSIOLOGY AND APPROACH TO CHELATION MANAGEMENT

    Athanasios Aessopos, Vasilios Berdoukas
    e2009002
    2009-07-18
    1594
    PDF: 486
    HTML: 1444
  • EFFECTS OF THALIDOMIDE ON ENDOTHELIAL ACTIVATION AND STRESS INDEX IN CHILDREN WITH Β-THALASSEMIA MAJOR

    Kun Yang
    e2024076
    2024-10-31
    https://doi.org/10.4084/MJHID.2024.076
    1066
    PDF: 579
    HTML: 150
  • CHARACTERIZATION AND ANTIMICROBIAL SUSCEPTIBILITY PROFILE OF SEPTICAEMIA-CAUSING PATHOGENS ISOLATED FROM FEBRILE CHILDREN WITH SICKLE CELL DISEASE IN KANO, NIGERIA.

    Ibrahim Yusuf
    e2018016
    2018-02-15
    https://doi.org/10.4084/mjhid.2018.016
    2886
    PDF: 981
    HTML: 523
  • Luspatercept Treatment in a β-Thalassemia Patient with Pulmonary Arterial Hypertension: A Case Report

    beibei yang, dongmei liu, changyu yang, Yali zhou, Guiping Liao, jian huang, Yingying Li, yinjiang tang, xiaolin yin
    e2025059
    2025-08-31
    https://doi.org/10.4084/MJHID.2025.059
    1127
    PDF: 554
    Html: 154
  • The EVOLVING ROLE OF HAEMATOLOGY NURSING PRACTICE: A CROSS-SECTIONAL SURVEY

    Sarah Liptrott, Mairéad NíChonghaile, Liz O'Connell, Erik Aerts
    e2023033
    2023-04-28
    https://doi.org/10.4084/MJHID.2023.033
    1880
    Suppl. Files: 889
    HTML: 436
    PDF: 750
  • Clinical and laboratory features of Hemoglobin La Desirade variant in association with sickle cell and alpha thalassemia genes Clinical & laboratory features of Hb La Desirade trait and compound heterozygous for Hb La Desirade and HbS Hemoglobin.

    Salam Alkindi, Shoaib Al Zadjali, Mohamed Al Rawahi , Hamoud Al Haddabi, Shahina Daar, Refaat Abdullah Elsadek, Bahaa Eldeen Diab Sherkawy, Anil Pathare
    e2021010
    2021-01-01
    https://doi.org/10.4084/mjhid.2021.010
    1622
    PDF: 473
    HTML: 249
  • IRON CHELATION THERAPY IN THALASSEMIA SYNDROMES

    Paolo Cianciulli
    e2009034
    1272
    PDF: 617
    HTML: 2320
  • HB H DISEASE CAUSED BY UNIPARENTAL DISOMY: FIRST REPORT OF THE αT-SAUDIΑ MUTATION IN THE CHINESE POPULATION

    Ge Wang, Hongting Xie, Jun Zhang, Peng Huang, Min Liang, Dina Zhu, Qianqian Zhang, Yuqiu Zhou, Xuan Shang
    e2024069
    2024-08-31
    https://doi.org/10.4084/MJHID.2024.069
    1035
    PDF: 610
    Html: 122
    Suppl. Files: 447
  • A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β⁺-Thalassaemia Patient

    Marta Bortolotti, Gianluca Costamagna, Marta Mancarella, Delia Gagliardi, Silvia Lanfranconi, Alessia Marcon, Margherita Migone De Amicis, Nereo Bresolin, Stefania Corti, Giovanna Graziadei
    e2022019
    2022-02-27
    https://doi.org/10.4084/MJHID.2022.019
    998
    PDF: 544
    HTML: 247
  • Clinical spectrum and genotypes of children with alpha-thalassemia in northeastern, Thailand

    Patcharee Komvilaisak, Nattakarn Sangkha, Arunee Jetsrisuparp, Kunanya Suwannaying, Goonnapa Fucharoen, Napat Laoaroon
    e2025081
    2025-10-31
    https://doi.org/10.4084/MJHID.2025.081
    305
    PDF: 217
    Html: 74
  • ASSOCIATION OF VDBP RS4701 VARIANT, BUT NOT VDR/RXR-? OVER-EXPRESSION WITH BONE MINERAL DENSITY IN PEDIATRIC ?-THALASSEMIA PATIENTS Vitamin D metabolic axis and BMD in ?-thalassemia

    Shaimaa Sahmoud, Mostafa S. Ibrahim, Eman A. Toraih, Noha Kamel, Manal Fawzy, Samar Elfiky
    e2020037
    2020-06-28
    https://doi.org/10.4084/mjhid.2020.037
    1256
    PDF: 734
    HTML: 210
  • BETA-GLOBIN GENE MUTATIONS IN TURKISH CHILDREN WITH BETA-THALASSEMIA: RESULTS FROM A SINGLE CENTER STUDY

    Ali Fettah, Cengiz Bayram, Nese Yarali, Pamir Isik, Abdurrahman Kara, Vildan Culha, Bahattin Tunc
    e2013055
    2013-09-02
    https://doi.org/10.4084/mjhid.2013.055
    1664
    PDF: 696
    HTML: 1641
    Beta-globin Gene Mutations in Turkish Children with Beta-Thalassemia: Results from a Single Center Study: 187
  • ALLOIMMUNIZATION IN PATIENTS WITH SICKLE CELL DISEASE AND THALASSAEMIA: EXPERIENCE OF SINGLE CENTRE FROM OMAN

    Anil Pathare, Salam Alkindi
    e2017013
    2017-02-15
    https://doi.org/10.4084/mjhid.2017.013
    2753
    PDF: 1285
    HTML: 1833
  • THALASSAEMIA INTERMEDIA : AN UPDATE

    Ali Taher, Khaled M. Musallam, Maria Domenica Cappellini
    e2009004
    2009-08-17
    1071
    PDF: 441
    HTML: 9445
  • PREVALENCE AND AETIOLOGY OF BACTEREMIA IN FEBRILE CHILDREN WITH SICKLE CELL DISEASE AT A NIGERIA TERTIARY HOSPITAL

    Biobele Jotham Brown, Hannah O Dada-Adegbola, Catherine Trippe, Olufunmilayo Olopade
    e2017039
    2017-06-20
    https://doi.org/10.4084/mjhid.2017.039
    2974
    PDF: 1266
    HTML: 1014
  • PREDISPOSING FACTORS TO INFECTIONS IN THALASSEMIA SYNDROME PATIENTS

    Eman M Mansory, Lina M. Abdulrahman, Balsam Osman, Sawsan M. Sawsan, Assil F. Ruckn, Marwa Aljedaani, Nemmat Hassan, Ahmed S. Barefah, Hatem M. Alahwal, Yassir Daghistani, Salem M. Bahashwan, Abdullah T. Almohammadi, Osman O. Radhwi
    e2025055
    2025-08-31
    https://doi.org/10.4084/MJHID.2025.055
    1693
    PDF: 1461
    HTML: 350
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